<原著>結節性硬化症あるいはvon Recklinghausen神経線維腫症を伴わない網膜のastrocytoma : 症例報告と文献的考察

概要

論文の詳細を見る
An extremely rare case of retinal astrocytoma not associated with tuberous sclerosis nor von Recklinghausen's neurofibromatosis is described. The patient, a 11-month-old female, suffered from esotropia. Upon examination, multicentric tumors were found in the bilateral fundus, and her left eyeball was enucleated from retinoblastoma. Macro-and microscopic observations of the enucleated left eye revealed three retinal tumors in the nerve fiber and ganglionic cell layers of the nerve head, equater and ora serrata. These were diagnosed as astrocytoma suspected to have originated from astrocytes in the nerve fiber layer of the retina. A search of the literature since 1934 revealed only 13 cases of retinal glioma not associated with tuberous sclerosis nor von Recklinghausen's neurofibromatosis (11 cases : astrocytoma, 2 cases : oligodendroglioma). Six of the 11 cases of astrocytoma were discovered in baby-and childhood, and all but the present case were unilateral and solitary.
近畿大学の論文
1983-12-25