軟部組織の好酸球肉芽腫とHistiocytosis Xによる尿崩症を合併したNoonan症候群の一例

概要

論文の詳細を見る
A case of diabetes insipidus, a Turner-featured 14 year-old boy, primarily due to histiocytosis X, which was histologically proved at the right radial bone, is reported. In addition to them, eosinophilic granuloma of the left parotid portion was also noted, which is characterized by so-called eosinophilic granuloma in the soft tissue or Kimura's disease. Histiocytosis X complicated with eosinophilic granuloma in the soft tissue and/or Noonan's syndrome is never been reported in the literature. Although it is noted here to differentiate eosinophilic granuloma in the soft tissue from histiocytosis X, the relationship of two diseases is suggested from this case. It should be more likely stated that Noonan's syndrome is accompanied by eosinophilic granuloma in the soft tissue and histiocytosis X with a rare incidence.
北里大学の論文
1973-10-31