Pulmonary Hypertension and Refractory Heart Failure in a Patient with Crow-Fukase (POEMS) Syndrome
スポンサーリンク
概要
- 論文の詳細を見る
We experienced the case of a 67-year-old man with refractory heart failure. He presented with dyspnea and progressive pitting edema of the lower limbs. Diuretics were insufficient to improve his symptoms. Cardiac catheterization demonstrated pulmonary hypertension. Additional examinations confirmed polyneuropathy, organomegaly, endocrinopathy and monoclonal gammopathy. The plasma vascular endothelial growth factor (VEGF) level was 1,340 pg/mL. The patient was diagnosed with Crow-Fukase (POEMS) syndrome. Echocardiography detected left ventricular hypertrophy and diastolic dysfunction. Polysomnography demonstrated severe sleep-disordered breathing. We herein describe a case of pulmonary hypertension with Crow-Fukase syndrome accompanied by left ventricular diastolic dysfunction and sleep-disordered breathing.
著者
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Ohkawara Hiroshi
Department Of Cardiology And Hematology Fukushima Medical University
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Noji Hideyoshi
Department Of Cardiology And Hematology Fukushima Medical University
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Ogawa Kazuei
Department Of Cardiology And Hematology Fukushima Medical University
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Kanno Yuki
Department Of Oral And Maxillofacial Surgery Faculty Of Medicine University Of Tokyo
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Mizukami Hiroyuki
Department Of Applied Electronics Tokyo Institute Of Technology:material Laboratory Research Divisio
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Kobayashi Atsushi
Department Of Applied Biological Science Tokyo University Of Agriculture And Technology
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Suzuki Hitoshi
Department Of Animal Science Faculty Of Agriculture Tohoku University
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Takahashi Hiroshi
Department Of Applied Aquabiology National Fisheries University
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SAITOH Shu-ichi
Department of Cardiology and Hematology, Fukushima Medical University
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Yoshihisa Akiomi
Department Of Advanced Cardiac Therapeutics Fukushima Medical University
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Takeishi Yasuchika
Department Of Advanced Cardiac Therapeutics Fukushima Medical University
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Nakazato Kazuhiko
Department Of Cardiology And Hematology Fukushima Medical University
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Shichishima-Nakamura Akiko
Department of Cardiology and Hematology, Fukushima Medical University
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Mizukami Hiroyuki
Department of Cardiology and Hematology, Fukushima Medical University, Japan
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Ogawa Kazuei
Department of Cardiology and Hematology, Fukushima Medical University, Japan
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Yokokawa Tetsuro
Department of Cardiology and Hematology, Fukushima Medical University, Japan
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Hisa Shinichi
Masu Memorial Hospital, Japan
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Saitoh Shu-ichi
Department of Cardiology and Hematology, Fukushima Medical University, Japan
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HISA SHINICHI
Masu Memorial Hospital
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Shichishima-Nakamura Akiko
Department of Cardiology and Hematology, Fukushima Medical University, Japan
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Noji Hideyoshi
Department of Cardiology and Hematology, Fukushima Medical University, Japan
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