脳動脈瘤を伴った多発性肝・腎のう胞症の2症例

概要

論文の詳細を見る
Since Borelius described in 1901 the first case of polycystic kidneys associated with intracranial aneurythm, a large number of cases have been reported in the literature from America and Europe. However a few reports has been seen in Japanese literature. 2 cases reported here, are much more complicated such as having combination of intracranial aneurythm and polycystic kidneys as well as polycystic liver in each cases. Case 1, 54 year-old housewife, was admitted because of hepatmegaly, enlargement of both kidneys, Honers sign on right side and diastolic hypertension, 190-104mmHg. In peritoneoscopic study multiple cysts were observed in the liver. Multiple cysts were also observed by I. V. P. and selective renal angiography. A left carotid arteriogram showed an aneurythm of left anterior cerebral artery. Diastolic hypertension were controled by spironolacton. After discharge, this case was died of subarachnoid hemorrhage. Case 2, 51 year-old male, with cerebral thrombosis of 10 years duration, came to this hospital for gouty attack. He was found renal enlargement and hepatmegaly, which were found polycystic kidneys and polycystic liver on ECHO gram and I. V. P.. A left carotid arteriogram showed an aneurythm of left middle cerebral artery. According to literature, most of the fatal cases are caused not only by renal failure and or hypertensive hemmorrage, but also by rupture of intracranial aneurythm.
北里大学の論文
1973-12-31