興味ある異常眼運動を呈した脊髄小脳変性症の1例--その神経耳科学的検討

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A 28-year-old woman with a slowly progressive ataxic gait was examined using routine neurological, CT scanning and equilibrium testing procedures. The following results were obtained:1) Neurological examinations and CT scanning revealed that symptoms were due to a dysfunction of the cerebellum with lesions of both the vermis and hemisphere.2) The spontaneous nystagmus tests revealed a peculiar nystagmus which was irregular and similar to a congenital nystagmus. Furthermore, the nystagmus altered its direction like a nystagmus alternans. A marked disturbance of the righting reflex, such as falling backwards was also observed.From the results described in (1) and (2), the following conclusions were drawn:(1) Symptoms were due to spino-cerebellar atrophy (Type of Déjèrine-Thomas), although the characteristics of spontaneous nystagmus were rather different from those of the nystagmus hitherto reported.(2) The nystagmus referred to herein was attributed to lesions of the brain stem. In contrast, disturbance of the body reflex was attributable to lesions of the cerebellum, particularly the vermis.
耳鼻咽喉科臨床学会の論文