肝血管腫の5症例--肝血管腫に伴うKasabach-Merritt症候群の本邦報告例の集計

概要

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5 cases of hepatic hemangioma were presented, of which one case with liver cirrhosis developed to Kasabach-Merritt syndrome after splenectomy. Eighteen cases including our case of Kasabach-Merritt syndrome in hepatic hemangioma have been reported in the Japanese literature up to date. Of sixteen cases 13 were cavernous hemangioma proved histologically. It is of interest that 17 of the 18 cases reported had anemia, of which 3 cases including our case had severe anemia due to microangiopathic hemolytic anemia. Hemostatic abnormalities were deteriorated or caused by either exploratory laparotomy or angiography in several cases. Therefore, one should keep in mind it in such procedures. Irradiation had no benificial effect for the regression of hemangioma. Among the diagnostic procedures, ultrasonography is the best way to determine the presence of hemangioma within the liver, while angiography is most useful diagnostic procedure to confirm the diagnosis.
社団法人日本肝臓学会の論文