C4B Deficiency Associated with Membranoproliferative Glomerulonephritis
スポンサーリンク
概要
- 論文の詳細を見る
A 10-year-old girl was noted to have microscopic hematuria and proteinuria in 1986. As her urinary abnormalities were persistent, she underwent a renal biopsy on 4 occasions until 2003. Although the appearances of the renal biopsies were strongly suspicious of systemic lupus erythematosus, she never exhibited specific autoantibodies or distinctive symptoms. She received corticosteroid therapy and the urinary findings responded. The 4th component of complement remained low during the period of the observation. Both genotyping and allotyping analysis revealed complete C4B deficiency. Some case reports have mentioned renal disease associated with C4B deficiency and we consider the nephropathy in this case to be related to the C4B deficiency.
著者
-
Terai Chihiro
Institute Of Rheumatology Tokyo Women's Medical College
-
Suzuki Koichi
Department Of Agro-bioscience Faculty Of Agriculture Iwate University
-
Yamada Shigeki
Department Of Biochemistry Research Laboratory Of Applied Biochemistry Tanabe Seiyaku Co. Ltd.
-
Terai Chihiro
Institute of Rheumatology, Tokyo Women's Medical University
-
TABEI Kaoru
Clinical Department of Internal Medicine, Jichi Medical School, Omiya Medical Center
-
TSUDA Tokutaro
Clinical Department of Internal Medicine, Jichi Medical School, Omiya Medical Center
-
MORIGUCHI Masato
Clinical Department of Internal Medicine, Jichi Medical School, Omiya Medical Center
-
ASANUMA Yu
Clinical Department of Internal Medicine, Jichi Medical School, Omiya Medical Center
-
IMAMURA Shigeki
Clinical Department of Internal Medicine, Jichi Medical School, Omiya Medical Center
-
TOYODA Akira
Clinical Department of Internal Medicine, Jichi Medical School, Omiya Medical Center
-
Asanuma Yu
Clinical Department of Internal Medicine, Jichi Medical School Omiya Medical Center
関連論文
- Dense deposit disease presenting as endocapillary proliferative nephritis
- Retinoic acid-inducible gene-I（ RIG-I） and diseases
- Renal Biopsy Findings in Children Receiving Long-Term Treatment with Cyclosporine A Given as a Single Daily Dose
- Effective Treatment with Cyclosporine A of a Child with Systemic Lupus Erythematosus Resistant to Cyclophosphamide Pulse Therapy
- Combined therapy of enalapril and losartan attenuates histologic progression in immunoglobulin A nephropathy
- Therapy-related membranous nephropathy in juvenile idiopathic arthritis with Turner syndrome
- Mizoribine oral pulse therapy for a patient with severe lupus nephritis
- End-Stage Kidney at the Onset of Nephrotic Syndrome in a 4-Year-Old Girl
- Acute renal failure due to hypertension : Malignant hypertension in an adolescent
- Disseminated candidiasis following prednisolone therapy in systemic lupus erythematosus
- Tubulointerstitial Nephritis and Uveitis Syndrome in Two Siblings
- Childhood idiopathic membranous glomerulonephritis with isolated antinuclear antibody positivity
- The characteristics of relapse in adult-onset minimal-change nephrotic syndrome
- Acute renal failure in a patient with hemophagocytic syndrome
- Renal function estimated from serum creatinine is overestimated in patients with rheumatoid arthritis because of their muscle atrophy
- Assessment of Coronary Artery Calcification in Hemodialysis Patients Using Multi-Detector Spiral CT Scan
- DEVELOPMENT AND EVALUATION OF A NEW PERORAL TEST AGENT GA-TEST FOR ASSESSMENT OF GASTRIC ACIDITY
- Intravenous Methylprednisolone Reduces the Risk of Propofol-Induced Adverse Effects During Wada Testing
- Thrombotic Stroke in a Child with Diarrhea-Associated Hemolytic-Uremic Syndrome with a Good Recovery
- Dermatomyositis associated with autoimmune idiopathic thrombocytopenia and anti-Ku antibody
- Progressive Interstitial Renal Fibrosis Due to Chinese Herbs in a Patient with Calcinosis Raynaud Esophageal Sclerodactyly Telangiectasia (CREST) Syndrome
- Antiphospholipid syndrome with complete abdominal aorta occlusion and chondritis
- Guillain-Barre syndrome accompanied by central nervous system lupus in a patient with juvenile rheumatoid arthritis
- Geoelectrical survey applied to estimate the groundwater flow direction between Payatas landfill and La Mesa Reservoir in Quezon City, Philippines
- C4B Deficiency Associated with Membranoproliferative Glomerulonephritis
- One third of Japanese patients with rheumatoid arthritis use complementary and alternative medicine
- Dose-response relationship of N-methyl-N-nitrosourea in inducing micrencephaly in mouse off-spring (NEREVOUS SYSTEM) (GENERAL SESSION BY POSTER PRESENTATION) (Proceedings of the 30th Annual Meeting)
- Organization and Primary Sequence of Multiple Genes Encoding Type II mRNA Species of Rice Prepro-glutelin(Biological Chemistry)
- Carcinoma of the gallbladder and anomalous arrangement of the pancreaticobiliary ductal system : Cell kinetic studies of gallbladder epithelial cells
- Differential Image Analysis of Proliferating Cell Nuclear Antigen (PCNA) Expression Level during Experimental Thyroid Carcinogenesis
- Blocking of monocyte chemoattractant protein-1 (MCP-1) activity attenuates the severity of acute pancreatitis in rats
- ベトナムにおけるハンセン病の現状-偏見差別の減少
- Identification of Novel tissue-specific Proteins in the Suboesophageal Body of the Silkworm, Bombyx mori
- A Reference Value for Delta-Aminolevulinic Acid in Plasma in the Population Occupationally Unexposed to Lead
- Subsequent Progression to Membranous Glomerulonephritis Following Exacerbation of Urticarial Rash in Systemic Lupus Erythematosus : Report of 2 Cases
- Possibly Simultaneous Primary Aldosteronism and Preclinical Cushing's Syndrome in a Patient with Double Adenomas of Right Adrenal Gland
- Progressive Glomerulonephritis with Increasing Proteinuria Induced by a Second Attack to the Mesangial Cell
- Early Intervention in Reducing Dietary Protein Intake Ameliorates Irreversible Mesangioproliferative Glomerulonephritis in Rats
- Incidence of Bladder Cancer Discovered by Urethrocystoscopy at Prostate Biopsy : Extraordinary High Incidence of Tiny Bladder Cancer in Elderly Males
- Autopsy findings of patients with urological neoplasms
- Fulminant second-set allograft rejection and endoscopic findings following small bowel transplantation in the rat
- Immunohistochemical Localization of Copper-Zinc and Manganese Superoxide Dismutases in Human Tissues
- Immunohistochemical localization of superoxide dismutase (SOD) in the background lesions of diisopropanolnitrosamine (DIPN) induced rat thyroid tumor
- Possible involvement of calcineurin, protein kinase C, and Src-family kinases in angiotensin II-induced tyrosine phosphorylation of p130^ in rat cardiac muscle
- Baculovirus-Mediated Production and Antifungal Activity of a Diapause-Specific Peptide, Diapausin, of the Adult Leaf Beetle, Gastrophysa atrocyanea : Coleoptera : Chrysomelidae
- A specific peptide produced during adult diapause of the leaf beetle, Gastrophysa atrocyanea Motschulsky (Coleoptera : Chrysomelidae)
- Benefits of Once-Daily Administration of Cyclosporine A for Children with Steroid-Dependent, Relapsing Nephrotic Syndrome
- Aspergillus oryzae palB^ Encodes a Calpain-Like Protease : Homology to Emericella nidulans PalB and Conservation of Functional Regions
- TED-AJ03-106 HIGH HEAT FLUX COOLING FOR ELECTRONIC DEVICES BY SUBCOOLED FLOW BOILING WITH MICROBUBBLE EMISSION
- Clinical pathway for tension-free vaginal mesh procedure : Evaluation in 300 patients with pelvic organ prolapse
- Overactive bladder and glaucoma : A survey at outpatient clinics in Japan
- Functional Mimicry of the Silkworm Diapause Hormone by an Insect Paralytic Peptide
- A Double Chaperone Function of the sHsp Genes against Heat-Based Environmental Adversity in the Soil-Dwelling Leaf Beetles
- H305 FUNCTIONAL ANALYSIS OF AN ADULT DIAPAUSE-ASSOCIATED PROTEIN FROM THE LEAF BEETLE GASTROPHYSA ATROCYANEA
- Antheraea yamamai Paralytic Peptide Induces Egg Diapause as Well as Larval Paralysis in Bombyx mori : the Primary Sequence-Activity Correlations
- Dissociation of m-Calpain Subunits Occurs after Autolysis of the N-Terminus of the Catalytic Subunit, and Is Not Required for Activation
- Autolysis of Calpain Large Subunit Inducing Irreversible Dissociation of Stoichiometric Heterodimer of Calpain
- Postmortem Molecular Screening for Cardiac Ryanodine Receptor Type 2 Mutations in Sudden Unexplained Death : R420W Mutated Case With Characteristics of Status Thymico-Lymphaticus
- Fatality due to acute fluoride poisoning in the workplace
- Analysis of two types of novel alleles in the DXS10011 locus
- Sequence analysis of two de novo mutation alleles at the DXS10011 locus
- Sibling incest and formulation of paternity probability : case report
- Haplotype analysis of a de novo allele at a vWF STR locus using flanking STR loci
- Estimation of Age from the Femur of Japanese Cadavers
- Distribution of Transforming Growth Factor-β and Its Receptors in Gastric Carcinoma Tissue
- Identification of an Imidazole Compound-Binding Protein from Diapausing Pharate First Instar Larvae of the Wild Silkmoth Antheraea yamamai
- Slit diaphragm dysfunction in proteinuric states : identification of novel therapeutic targets for nephrotic syndrome
- Unilateral Active Adrenal Tuberculosis Featuring Persistent Intermittent Fever
- Isolation and Characterization of a 41 kDa Sericin from the Wild Silkmoth Antheraea yamamai
- Study on Slope Erosion by Simulated Rainfall
- BIOLOGICAL IMPEDIMENT TO OXYGEN SENSING IN INJURED PULMONARY MICROCIRCULATION EXPOSED TO HIGH OXYGEN ENVIRONMENT
- Clinical analysis of multibacillary leprosy patients after 1-year fixed World Health Organization recommended multidrug therapy at Yangon General Hospital, Myanmar
- STUDY ON CHARACTERISTICS OF RESERVOIR SEDIMENTATION WITH HYDRAULIC JUMP
- Cytotoxic Activity in the Colleterial Glands of Antheraea yamamai against Rat Hepatoma Cells
- Reduced urinary 6β-hydroxycortisol to cortisol rations in patients with liver cirrhosis
- Genetic studies of eight X-STRs in a Japanese population
- In vitro pharmacological activities of the extracts from red ant Formica aquilonia as potential therapeutic agents
- Localization of CORO1A in the Macrophages Containing Mycobacterium leprae
- Continuous rearing of an entomoresource, the leaf beetle, Gastrophysa atrocyanea Motschulsky (Coleoptera : Chrysomelidae) on artificial diets
- Growth Suppression of Rat Hepatoma Cells by a Pentapeptide from Antheraea yamamai
- MATLAB Implementation of a Genetic Algorithm for Linearly Constrained Optimization Problems
- Eosinophilic Fasciitis Complicated with Peripheral Polyneuropathy
- Co-expression of vascular endothelial growth factor and its receptor, neuropilin-1, in a B cell lymphoma cell line (OHK) with primary effusion lymphoima immunophenotype
- Evaluation of polymerase chain reaction-based detection of Mycobacterium leprae for the diagnosis of leprosy
- Polymorphisms of p21 cyclin-dependent kinase inhibitor and malignant skin tumors
- Pseudo-Critical Heat Capacity of Single Lipid Bilayers
- E204 SUBCOOLEO FLOW BOILING OF WATER IN A HORIZONTAL CHANNEL : Bubble behavior and heat flux in transition boiling(Boiling two-phase flow)
- Nucleotide and Deduced Amino Acid Sequences of a cDNA Encoding a Lipocalin Protein in the Central Nervous System of Bombyx mori
- The Evidence for Adjuvant Treatment of Elderly Patients (Age≧70) with Stage III Colon Cancer Is Inconclusive
- Absorption of Fertilizer and Soil Nitrogen by Rice Plants under the Various Cultural Conditions of Different Paddy Fields. I. Relationships between the Rate of Basal Nitrogen and Nitrogen Absorption by Rice Plants.
- Morphological Changes of Human Myeloid Leukemia K562 Cells by a Protein Phosphatase Inhibitor, Tautomycin
- Effects of Imidazole Compounds on Control of Life Cycle of the Wild Silkmoth, Antheraea yamamai
- Postmortem molecular analysis for fatal arrhythmogenic disease in sudden unexplained death
- ABO blood group alleles and genetic recombination
- Postmortem genetic analysis for a sudden death case complicated with Marfan syndrome
- The changes of regional cerebral blood flow with advancing age in normal children
- Protein-losing Enteropathy Associated with Immune Complex-mediated Vasculopathy in a Case of Undifferentiated Connective Tissue Disease
- Photoelectrochemical Hydrogen Production by a Photocell Using the Phytolacca americana Photosystem I Particles-Methylviologen System
- Leprosy situation in Vietnam-reduced burden of stigma
- Intramolecular Hydrogen Bonds. XVII. Intramolecular Hydrogen Bonding Involving the Mercapto Group as a Hydrogen Donor