Benign Premature Ventricular Complexes from the Right Ventricular Outflow Tract Triggered Polymorphic Ventricular Tachycardia in a Latent Type 2 LQTS Patient
スポンサーリンク
概要
- 論文の詳細を見る
A 57-year-old woman showed frequent premature ventricular complexes (PVCs) originating from the right ventricular outflow tract (RVOT), and some of the PVCs triggered polymorphic ventricular tachycardia (PVT). Structural heart diseases were ruled out by conventional cardiac examinations. Radiofrequency catheter ablation was successful in eliminating the PVCs and subsequent PVT. However, epinephrine infusion unmasked her prolonged QT interval, and a genetic analysis revealed a KCNH2 mutation (R694H) as the cause of latent type-2 long QT syndrome (LQTS). This case suggests that latent LQTS may work as an arrhythmogenic substrate of PVT triggered by a benign form of RVOT-PVCs in patients with a structurally normal heart.
著者
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Sato Akinori
Division of Cardiology, Niigata University Graduate School of Medical and Dental Sciences
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Furushima Hiroshi
Division Of Cardiology Hemotology And Endocrinology Niigata University Graduate School Of Medical An
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Chinushi Masaomi
School Of Health Science Niigata University School Of Medicine
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Izumi Daisuke
Division Of Cardiology Niigata University Graduate School Of Medical And Dental Science
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Abe Akira
Department Of Internal Medicine Nephrology Division University Of Michigan
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Sonoda Keiko
Division of Cardiology, Niigata University Graduate School of Medical and Dental Sciences
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Izumi Daisuke
Division of Cardiology, Niigata University Graduate School of Medical and Dental Sciences, Japan
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Sonoda Keiko
Division of Cardiology, Niigata University Graduate School of Medical and Dental Sciences, Japan
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Abe Akira
Department of Cardiology, Niigata Minami Hospital, Japan
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