Idiopathic Portal Hypertension in a Patient with Mixed Connective Tissue Disease and Protein C Deficiency
スポンサーリンク
概要
- 論文の詳細を見る
We report a 29-year-old woman with a 2.5 year history of mixed connective tissue disease (MCTD) who developed idiopathic portal hypertension (IPH) and thrombocytopenia as a result of hypersplenism. She had recurrent esophagogastric variceal rupture. Hematological examination also revealed low levels of protein C activity. The liver biopsy specimen showed non-specific mild inflammation and no thrombi. However, portal vein thrombosis developed after splenectomy. This was a rare case of severe complications of IPH accompanying MCTD and protein C deficiency.
著者
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Horai Yoshiro
Department of Internal Medicine and Rheumatology, Clinical Research Center, National Hospital Organi
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Suematsu Eiichi
Department Of Internal Medicine And Rheumatology Clinical Research Institute National Hospital Organ
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Ando Hitoshi
Department Of Biomaterials Science Faculty Of Dentistry Tokyo Medical And Dental University
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Miyamura Tomoya
Department Of Internal Medicine And Rheumatology Clinical Research Institute National Hospital Organ
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Minami Rumi
Department Of Internal Medicine And Rheumatology Clinical Research Institute National Hospital Organ
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Nakamura Masataka
Department Of Chemical Science And Engineering Graduate School Of Engineering Kobe University
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Hirata Akie
Department Of Internal Medicine And Rheumatology Clinical Research Institute National Hospital Organ
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Yamamoto Masahiro
Department Of Agricultural Chemistry Faculty Of Agriculture Niigata University
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Takahama Soichiro
Department of Immunology and Infectious Diseases, Clinical Research Institute, Kyushu Medical Center, National Hospital Organization
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Horai Yoshiro
Department of Internal Medicine and Rheumatology, Clinical Research Center, National Hospital Organization Kyushu Medical Center
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Miyamura Tomoya
Department of Internal Medicine and Rheumatology, Clinical Research Center, National Hospital Organization Kyushu Medical Center
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Minami Rumi
Department of Internal Medicine and Rheumatology, Clinical Research Center, National Hospital Organization Kyushu Medical Center
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Minami Rumi
Department of Immunology and Infectious Diseases, Clinical Research Institute, Kyushu Medical Center, National Hospital Organization
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Suematsu Eiichi
Department of Internal Medicine and Rheumatology, Clinical Research Center, National Hospital Organization Kyushu Medical Center
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