症例報告 The first Japanese case report of closing gastroschisis

概要

論文の詳細を見る
Gastroschisis is a rare congenital anomaly that results in an abdominal wall defect. Closing gastroschisis is a pathological condition in which the abdominal wall has closed, and the intestinal tubes become strangulated at the umbilicus. All known cases of closing gastroschisis have been reported from the United States and Europe. As of 2008, only 50 cases of closing gastroschisis have been reported in the English literature. Here, we report the first case from Asia. A newborn boy (2,664g) was delivered at the gestational age of 38 weeks and 2 days. A stick-like solid mass was found on his abdomen at birth, and we diagnosed the condition as congenital atresia of the jejunum and colon with short bowel syndrome. The patient was 17 months of age at the time of this report and continues to require parenteral nutritional support. Surgery involving an intestinal lengthening procedure is considered to be required in the future.
2010-04-20