姉妹に発現した基底細胞母斑症候群の 2 例

概要

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Two cases of basal cell nevus syndrome are reported. Both cases were referred for evaluation of multiple radiolucent jaw lesions. In the case of a 20-year-old female, multiple jaw cysts, a broad nasal root, ocular hypertelolism, frontal bossing, several bifid ribs, calcification of the falx cerebri and pit of palm were presented. In the other case, her younger sister, a 13-year-old female, had findings same as her sister. Both cases had many features of basal cell nevus syndrome. Histopathological diagnosis of multiple jaw cysts was odontogenic keratocyst in both cases. Both cysts were enucleated. Recurrence of cysts are not seen, but we think it necessary to have a long term follow up.
九州歯科学会の論文
1989-12-25