Porphyria Cutanea Tarda with Constrictive Pericarditis in a Family.
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概要
- 論文の詳細を見る
Two cases of familial porphyria cutanea tarda (PCT) with constrictive pericarditis are described. A 50-year-old woman and her 48-year-old younger brother were admitted because of right ventricular heart failure. Constrictive pericarditis was diagnosed by RV pressure waveform and echocardiogram. The patients were diagnosed as PCT based on clinical symptoms, histologic findings and elevated urinary excretion levels of uroporphyrin. Even to this day, over 40% of the etiology of constrictive pericarditis remains unknown. There is a possibility of overlooking porphyria cutanea tarda in constrictive pericarditis patients. This report describes the first documented cases of famil-ial PCT with constrictive pericarditis.
- International Heart Journal刊行会の論文
著者
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Shirai Toshizumi
Department Of Thoracic Surgery Ome Municipal General Hospital
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Marumo Fumiaki
Second Department Of Internal Medicine Faculty Of Medicine Tokyo Medical And Dental University
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Adachi Susumu
Second Department of Internal Medicine, Tokyo Medical and Dental University
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Amano Jun
Department Of Cardio-thoracic Surgery Juntendo Univ. School Of Med. Tokyo Med.& Dent- Univ.
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Yajima Takashi
Department Of Internal Medicine Musashino Red-cross Hospital
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Miyahara Yasuhiro
Department Of Internal Medicine Kashiwa City Hospital
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Ito Hiroshi
Second Department Of Internal Medicine Tokyo Medical And Dental University
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Hiroe Michiaki
Second Department Of Internal Medicine
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YAJIMA Takashi
Department of Internal Medicine, Hokushin General Hospital
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MIYAHARA Yasuhiro
Department of Internal Medicine, Hokushin General Hospital
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