同側肺葉内転移をみた,肺原発小児横紋筋肉腫の1例

概要

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Three-year-old girl complained fever, caugh, dyspnea and chest pain. Plain chest X-ray film on admission showed a mass in the left lower lung area and a coin lesion in the upper area of the same lung. The left lower lobe was occupied by a huge tumor which was resected and a single mass locating in the upper lobe was enucleated. Both of these tumors were histologically proved to be rhabdomyosarcoma, pleomorphic subtype. She has been treated with pulse VAC and adriamycin and has now been free from disease for seven months since surgery. A mass in the left upper lobe was supposed to be a matastasis from the lower lobe. Rhabdomyosarcoma originating from the lung is quite rare and only nine cases have been reported in the literature. Furthermore, this case is quite characteristic in histology and the site of metastasis. Reviewing the past reports, rhabdomyosarcoma in children were embryonic subtype in histology and the metastases were found in the following frequency; lymph nodes (33%), central nervous system (19%), liver (14%), the other side of the lung (10%). Our case will be the first report of a solitary metastasis to the ipsilateral lung.
日本小児外科学会の論文
1987-12-20