両側高度感音難聴を合併した川崎病例

概要

論文の詳細を見る
Kawasaki disease (KD) is an idiopathic systemic vasculitis common in infants and children that affects predominantly small and medium-sized extraparenchymal muscular arteries. KD manifests various clinical symptoms, of which coronary aneurysms are the most important complication. However, the association of sensorineural hearing loss with KD is rare. A 7-year-old girl with KD was referred to our department with a chief complaint of hearing loss. In her hearing test, she showed a high degree of bilateral sensorineural hearing loss. Although the patient was treated with steroid pulse therapy (methylprednisolone), her hearing level deteriorated. Two weeks after steroid therapy, a slight improvement was seen. Thereafter, the patient started to use hearing aids. About one year has elapsed since the onset of hearing loss, but her hearing level has not improved.