Successful Treatment of Heart Failure in an Adult Patient with Prader-Willi Syndrome
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概要
- 論文の詳細を見る
Prader-Willi Syndrome (PWS) is a rare genetic disorder characterized by physical, psychological and physiological abnormalities. Obesity and related cardiovascular diseases are a common problem in adult patients with PWS. This report describes a case of adult PWS with heart failure associated with marked obesity and sleep-disordered breathing that was successfully treated with oxygen therapy, adaptive servoventilation, medications, diet therapy and rehabilitation.
著者
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Hayano Motonobu
Department of Cardiology
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Maemura Koji
Department Of Cardiovascular Medicine Course Of Medical And Dental Sciences Graduate School Of Biome
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Kawano Hiroaki
Department Cardiovascular Medicine Kumamoto University:division Of Intensive Care Unit Kumamoto Univ
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Matsumoto Yuji
Department Of Biomaterials Science Graduate School Of Agricultural And Life Sciences The University
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Arakawa Shuji
Department Of Cerebrovascular Disease Hakujyuji Hospital
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Shimazaki Koichi
Department of Rehabilitation, Nagasaki Rosai Hospital, Japan
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Ikeda Tooru
Department of Internal Medicine, Nagasaki Rosai Hospital, Japan
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