Desmoplastic Small Round Cell Tumors in a Young Man
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概要
- 論文の詳細を見る
A previously healthy 18-year-old man was admitted to our hospital with abdominal pain in September 2010. We performed a percutaneous biopsy of multiple intrahepatic masses. A diagnosis of desmoplastic small round cell tumors was confirmed based on the presence of a polyphenotypic immunoprofile (positivity for EMA, vimentin, cytokeratin, desmin and WT1) and characteristic EWS-WT1 gene fusion. Because the mass had invaded the mesentery and the disease had disseminated to liver, the patient received palliative chemotherapy with carboplatin, paclitaxel, vincristine, doxorubicin, cyclophosphamide, ifosfamide, etoposide and irinotecan. The maximal response to the chemotherapy was a partial remission. The patient died 20 months after diagnosis.
著者
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Irie Makoto
Department Of Gastroenterology And Medicine Faculty Of Medicine Fukuoka University
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Sohda Tetsuro
Department Of Gastroenterology And Medicine Faculty Of Medicine Fukuoka University
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Nabeshima Kazuki
Department Of 2nd Pathology Miyazaki Medical College
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Takamatsu Yasushi
Department Of Internal Medicine Miyazaki Prefectural Hospital
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Aoki Mikiko
Department Of Pathology Faculty Of Medicine Fukuoka University
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Tamura Kazuo
Department Of Hematology Harasanshin General Hospital
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Sakisaka Shotaro
Department Of Gastroenterology And Hepatology Fukuoka University School Of Medicine
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Hirano Genryu
Department Of Gastroenterology Fukuoka City Medical Association Hospital
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Tanaka Toshihiro
Department Of Applied Chemistry Graduate School Of Engineering Osaka City University
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Shakado Satoshi
Department Of Gastroenterology And Medicine Faculty Of Medicine Fukuoka University
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Nakashima Yuta
Department of Medical Oncology, Hematology and Infectious Disease, Fukuoka University Faculty of Medicine, Japan
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Takamatsu Yasushi
Department of Medical Oncology, Hematology and Infectious Disease, Fukuoka University Faculty of Medicine, Japan
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Irie Makoto
Department of Gastroenterology and Medicine, Fukuoka University Faculty of Medicine, Japan
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Sakisaka Shotaro
Department of Gastroenterology and Medicine, Fukuoka University Faculty of Medicine, Japan
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Shakado Satoshi
Department of Gastroenterology and Medicine, Fukuoka University Faculty of Medicine, Japan
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Nabeshima Kazuki
Department of Pathology, Fukuoka University Faculty of Medicine, Japan
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Hirano Genryu
Department of Gastroenterology and Medicine, Fukuoka University Faculty of Medicine, Japan
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