CARDIOVASCULAR FINDINGS IN FAMILIAL HYPERCHOLESTEROLEMIC CHILDREN
スポンサーリンク
概要
- 論文の詳細を見る
Four child patients (1 male and 3 females) with homozygous familial hypercholesterolemia (FH) were examined. They were 4y4m to 9y8m of age on admission. A female patient at age 5y7m on admission had already experienced anginal attacks. Ischemic change was found on exercise ECG in 2 patients. Grade 1/6 to 3/6 (Levine) systolic ejection type murmur was audible in all patients. Cardiac catheterization was carried out in all patients. Supravalvular aortic stenosis was found and so-called atherosclerotic wall thickening was also noticed in 3 of them. Narrowing of the coronary arteries was found in only l patient who complained of anginal pain. Supravalvular aortic stenosis was more prevalent than coronary artery disorders in FH children and this lesion was also detected by echocardiography. Therefore. follow-up by echocardiography seems to be very useful in assessing the progression of atherosclerosis in patients with severe hypercholesterolemia.
- 社団法人日本循環器学会の論文
- 1991-02-20
著者
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Fujita Tsuyoshi
Department Of Cardiology Tokyo Women's Medical Univercity
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YAMAMOTO Akira
Department of Biopharmaceutics, Kyoto Pharmaceutical University
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HORIGUCHI YASUNORI
Department of Pediatrics, Kitasato University School of Medicine
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KAMIYA TETSURO
The Department of Pediatrics. National Heart Institute. Osaka
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Kamiya Tetsuro
The Department Of Pediatrics National Cardiovascular Center
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Horiguchi Yasunori
Departlnent Of Pediatrics Kitasato University School Of Medicine
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Fujita Tsuyoshi
Department Of Cardiology The Heart Institute Of Japan Tokyo Women's Medical University
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Arakaki Yoshio
The Department Of Pediatrics National Cardiovascular Center
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YAZAWA KEN-ICHI
The Department of Pediatrics, National Cardiovascular Center
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Yazawa Ken-ichi
The Department Of Pediatrics National Cardiovascular Center
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Yamamoto Akira
Department Of Biopharmaceutics Kyoto Pharmaceutical University
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Fujita Tsuyoshi
Department Of Surgery National Cardiovascular Center
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Yamamoto Akira
Department Of Anatomy School Of Medicine University Of Tokushuma
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Yamamoto Akira
Department Of Etiology And Pathophysiology National Cardiovascular Center Research Institute
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Fujita Tsuyoshi
Department Of Cardiac Surgery. National Cardiovascular Center Hospital
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Yamamoto Akira
Department Of Anatomy School Of Medicine University Of Tokushima
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