Surgical Treatment for Scheie's Syndrome(Mucopolysaccharidosis Type I-S) : Report of Two Cases
スポンサーリンク
概要
- 論文の詳細を見る
Scheie's syndrome(mucopolysaccharidosis type I-S)is a rare genetic lysosomal storage disease affecting mucopolysaccharide metabolism, and is known to include cardiovascular disease.Surgical treatment was carried out in 2 patients with Scheie's syndrome.Patient 1 was a 56-year-old man with triple-vessel coronary artery disease, who successfully underwent coronary artery bypass grafting.Patient 2 was a 52-year-old man with aortic and mitral valve stenosis, who successfully underwent combined aortic and mitral valve replacement.The literature on Scheie's syndrome associated with valvular and coronary artery disease is also reviewed.
- 社団法人日本循環器学会の論文
- 1998-08-20
著者
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MATSUMOTO Masahiko
Department of Biochemistry, School of Medicine, Tokai University
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Miwa Senri
Department of Cardiovascular Surgery, Kyoto University Graduate School of Medicine
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Matsumoto Masahiko
Department Of Biochemistry School Of Medicine Tokai University
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Konoshi Yutaka
Department Of Cardiovascular Surgery Japanese Red Cross Society Wakayama Medical Center
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Matsumoto Masahiko
Department Of Cardiovascular Surgery Japanese Red-cross Sociaty Wakayama Medical Center
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Minakata Kenji
Department of Cardiovascular Surgery, Japanese Red Cross Society Wakayama Medical Center
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Minakata Kenji
Department Of Cardiovascular Surgery Japanese Red-cross Sociaty Wakayama Medical Center
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Miwa Senri
Department Of Cardiovascular Surgery Japanese Red Cross Society Wakayama Medical Center
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Minakata Kenji
Department Of Cardiovascular Surgery Japanese Red Cross Society Wakayama Medical Center
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Konishi Yutaka
Department Of Cardiovascular Surgery Japanese Red-cross Sociaty Wakayama Medical Center
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