Two Siblings with Type 1 Autoimmune Pancreatitis
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概要
- 論文の詳細を見る
Type 1 autoimmune pancreatitis (AIP) is characterized by a high serum IgG4 concentration and is closely associated with the HLA-DRB1*04:05-DQB1*04:01 haplotype, for which family studies may disclose its immunogenetic significance. In the present study, we encountered two male siblings with type 1 AIP who exhibited diffuse pancreatic swelling with a capsule-like rim and diffuse pancreatic duct stricture. The younger brother also displayed characteristic IgG4-related sialadenitis and retroperitoneal fibrosis. Contrary to our expectations, the siblings showed only normal or slightly elevated values of serum IgG4 and no HLA DRB1*04:05-DQB1*04:01 haplotype, suggesting that type 1 autoimmune pancreatitis is associated with multiple immunogenetic factors.
著者
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Ota Masao
Department Of Legal Medicine Shinshu University School Of Medicine
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Kawa Shigeyuki
Center For Health Safety And Environmental Management Shinshu University
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Hamano Hideaki
Department Of Gastroenterology Shinshu University School Of Medicine
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Arakura Norikazu
Department Of Gastroenterology Shinshu University School Of Medicine
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Ito Tetsuya
Department Of Animal Science Obihiro University Of Agriculture And Veterinary Medicine
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Maruyama Masahiro
Department Of Applied Mathematics Faculty Of Engineering Science Osaka University
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Watanabe Takayuki
Department Of Biochemistry School Of Dentistry Hokkaido University
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Muraki Takashi
Department Of Gastroenterology Shinshu University School Of Medicine
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Ito Tetsuya
Department of Gastroenterology, Shinshu University School of Medicine, Japan
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Hamano Hideaki
Department of Gastroenterology, Shinshu University School of Medicine, Japan
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Kanai Keita
Department of Gastroenterology, Shinshu University School of Medicine, Japan
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Oguchi Takaya
Department of Gastroenterology, Shinshu University School of Medicine, Japan
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Arakura Norikazu
Department of Endoscopic Examination Center, Shinshu University School of Medicine, Japan
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Muraki Takashi
Department of Gastroenterology, Shinshu University School of Medicine, Japan
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