Improved Quality of Life and Unchanged Magnetic Resonance Brain Imaging After Living Donor Liver Transplantation for Late-Onset Ornithine Transcarbamylase Deficiency : Report of a Case
スポンサーリンク
概要
- 論文の詳細を見る
- 2005-12-01
著者
-
SATOMI SUSUMU
Division of Transplant Surgery, Tohoku University Graduate School of Medicine
-
Satoh Akira
Division of Cardiovascular Medicine, University of Tsukuba
-
OHURA Toshihiro
Department of Pediatrics, Tohoku University School of Medicine
-
KAWAGISHI Naoki
Division of Advanced Surgical Science and Technology, Graduate School of Medicine, Tohoku University
-
SATOH Kazushige
Division of Advanced Surgical Science and Technology, Graduate School of Medicine, Tohoku University
-
AKAMATSU Yorihiro
Division of Advanced Surgical Science and Technology, Graduate School of Medicine, Tohoku University
-
SEKIGUCHI Satoshi
Division of Advanced Surgical Science and Technology, Graduate School of Medicine, Tohoku University
-
FUJIMORI KEISEI
Division of Advanced Surgical Science and Technology, Tohoku University Graduate School of Medicine
-
ITO Tetsuya
Department of Physics and Research Center for the Early Universe, The University of Tokyo
-
Satoh Akira
Division Of Advanced Surgical Science And Technology Tohoku University Graduate School Of Medicine
-
Satoh Kazushige
Division Of Advanced Surgical Science And Technology Graduate School Of Medicine Tohoku University
-
ENOMOTO YOSHITAKA
Division of Advanced Surgical Science and Technology, Graduate School of Medicine, Tohoku University
-
TAKASAGO YUHEI
Pediatric Department, Morioka Children's Hospital
-
Sekiguchi Satoshi
Division Of Advanced Surgical Science And Technology Graduate School Of Medicine Tohoku University
-
Takasago Yuhei
Pediatric Department Morioka Children's Hospital
-
Ohura Toshihiro
Department Of Pediatrics Graduate School Of Medicine Tohoku University
-
Kawagishi Naoki
Division Of Advanced Surgical Science And Technology Graduate School Of Medicine Tohoku University
-
Satomi Susumu
Division Of Advanced Science And Technology Tohoku University Graduate School Of Medicine
-
Ito Tetsuya
Department Of Neonatology And Pediatrics Nagoya City University Graduate School Of Medical Sciences
-
Akamatsu Yorihiro
Division Of Advanced Surgical Science And Technology Graduate School Of Medicine Tohoku University
-
Enomoto Yoshitaka
Division Of Advanced Surgical Science And Technology Graduate School Of Medicine Tohoku University
-
Ito Tetsuya
Department Of Applied Chemistry Graduate School Of Science And Engineering Ehime University
-
Fujimori Keisei
Division Of Advanced Surgical Science And Technology Graduate School Of Medicine Tohoku University
-
Ito Tetsuya
Department Of Animal Science Obihiro University Of Agriculture And Veterinary Medicine
-
Ito Tetsuya
Department Of Pediatrics Nagoya City University Medical School
関連論文
- Living Related Liver Transplantation for Acute Fulminant Hepatitis B : Experience from Two Possible Hyper-Acute Cases
- PE-369 The Histological Findings of Vascular Response to Drug Eluting Stents(PE062,Atherosclerosis (Clinical/Treatment) (IHD),Poster Session (English),The 73rd Annual Scientific Meeting of The Japanese Circulation Society)
- The effects of copper-histidine therapy on brain metabolism in a patient with Menkes disease : a proton magnetic resonance spectroscopic study
- Long-term outcome of ABO-incompatible living-donor liver transplantation : a single-center experience
- Usefulness of beta-D glucan in diagnosing Pneumocystis carinii pneumonia and monitoring its treatment in a living-donor liver-transplant recipient
- Steroid-Resistant Late Acute Rejection after a Living Donor Liver Transplantation : Case Report and Review of the Literature
- A 350 GHz SIS Receiver on the Nobeyama 10m Submillimeter Telescope
- Abnormal white matter lesions with sensorineural hearing loss caused by congenital cytomegalovirus infection : retrospective diagnosis by PCR using Guthrie cards
- IL-10 and RANTES are Elevated in Nasopharyngeal Secretions of Children with Respiratory Syncytial Virus Infection
- High postnatal oxidative stress in neonatal cystic periventricular leukomalacia
- Rapid, simplified and sensitive method for screening fructose-1, 6-diphosphatase deficiency by analyzing urinary metabolites in urease/direct preparations and gas chromatography-mass spectrometry in the selected-ion monitoring mode
- Hypophosphatemia in juvenile patients with systemic lupus erythematosus
- Novel mutations in five Japanese patients with 3-methylcrotonyl-CoA carboxylase deficiency
- Gene Therapy for Pancreatic Cancer Using an Adenovirus Vector Encoding Soluble flt-1 Vascular Endothelial Growth Factor Receptor
- Steroid and xenobiotic receptor in human esophageal squamous cell carcinoma : A potent prognostic factor
- Immunohistopathological and molecular genetic features of a case in which gastrointestinal stromal tumor recurred five times
- The Relationship of Thyroid Cancer with Radiation Exposure from Nuclear Weapon Testing in the Marshall Islands
- Characteristics of Young-Onset Hypertension Identified by Targeted Screening Performed at a University Health Check-Up
- Acylcarnitine Profiles during Carnitine Loading and Fasting Tests in a Japanese Patient with Medium-Chain Acyl-CoA Dehydrogenase Deficiency
- Long-term Outcome after Living Donor Liver Transplantation for Two Cases of Homozygous Familial Hypercholesterolemia from a Heterozygous Donor
- Outcome of Laparoscopic Rectopexy for Complete Rectal Prolapse in Patients Older than 70 Years Versus Younger Patients
- Reduction in cerebral blood flow volume in infants complicated with hypoxic ischemic encephalopathy resulting in cerebral palsy
- Acid Sphingomyelinase : Relation of ^Lysine Residue on the Ratio of Intracellular to Secreted Enzyme Activity
- Ultrasonographic Findings in Neonates Screened for Congenital Hypothyroidism
- Molecular analysis of Japanese patients with steroid 21-hydroxylase deficiency
- Primitive Neuroectodermal Tumor as a Differential Diagnosis of CD56-Positive Tumors in Adults
- A possible mechanism of neonatal intrahepatic cholestasis caused by citrin deficiency
- Novel missense mutation (R94S) in the TAZ (G4.5) gene in a Japanese patient with Barth syndrome
- An undescribed subset of neonatal interahepatic cholestasis associated with multiple hyperaminoacidemia
- Risk Factors and Impact of β-D Glucan on Invasive Fungal Infection for the Living Donor Liver Transplant Recipients
- Two cases in one family of living donor liver transplantation for homozygous familial hypercholesterolemia
- Usage of Deoxyspergualin on Steroid-Resistant Acute Rejection in Living Donor Liver Transplantation
- Improved Quality of Life and Unchanged Magnetic Resonance Brain Imaging After Living Donor Liver Transplantation for Late-Onset Ornithine Transcarbamylase Deficiency : Report of a Case
- Hepatic resection of giant metastatic tumor from clear cell carcinoma of the ovary
- PE-473 Nocturnal Home Oxygen Therapy is Effective for Patients with Heart Failure Accompanying Pulmonary Disease(Heart failure, clinical-7 (M) PE79,Poster Session (English),The 70th Anniversary Annual Scientific Meeting of the Japanese Circulation Society
- Detection of Pivaloylcarnitine in Pediatric Patients with Hypocarnitinemia after Long-Term Administration of Pivalate-Containing Antibiotics
- Preoperative Radiation Therapy is an Independent and Strong Risk Factor for Late Non-cancer Death after Esophagectomy
- Severity of Virilization of External Genitalia in Japanese Patients with Salt-wasting 21-hydroxylase Deficiency
- OE-387 Impact of Higher Blood Pressure on the Risk of Death in 27-year Follow-up Study(Preventive medicine/Epidemiology/Education-1, The 71st Annual Scientific Meeting of the Japanese Circulation Society)
- FRS-039 High Serum Dehydroepiandrosteone Sulfate Levels are Strikingly Associated with Less Mortality in Men (27-year follow-up study)(Preventive Medicine, The 71st Annual Scientific Meeting of the Japanese Circulation Society)
- A Solitary Bronchial Papilloma with Malignant Changes
- Alteration of Ammonia and Carnitine Levels in Short-Term Treatment with Pivalic Acid-Containing Prodrug
- A case of holocarboxylase synthetase deficiency with insufficient response to prenatal biotin therapy
- Long follow up of betaine therapy in two Japanese siblings with cystathionine β-synthase deficiency
- Novel mutations in the cytochrome P450 2C19 gene : a pitfall of the PCR-RFLP method for identifying a common mutation
- A Simple Quantitative Assay for Urinary Adenosine Using Column-Switching High-Performance Liquid Chromatography
- Urinary uracil in female patients with ornithine transcarbamylase deficiency
- Multiple sclerosis with onset of cerebellar ataxia in an 18-month-old girl
- Vitamin B_6-Responsive Ornithine Aminotransferase Deficiency with a Novel Mutation G237D
- Treatment with L-Valine Ameliorates Liver Fibrosis and Restores Thrombopoiesis in Rats Exposed to Carbon Tetrachloride
- Liquid chromatographic-atmospheric pressure chemical ionization mass spectrometric analysis of glycine conjugates and urinary isovalerylglycine in isovaleric acidemia
- Histological findings in the livers of patients with neonatal intrahepatic cholestasis caused by citrin deficiency
- Differential Growth Properties of Normal and Malignant Esophageal Epithelial Cells : A Possible Cross Talk between Transforming Growth Factor-β1 and Epidermal Growth Factor Signaling
- Intravenous glycerol therapy should not be used in patients with unrecognized fructose-1, 6-bisphosphatase deficiency
- 二酸化炭素の銅担持ガス拡散電極による電気化学的大量還元-2-反応機構の提案
- Observation of ULF emissions Associated with Earthquakes
- Effects of fasting and refeeding on plasma concentrations of leptin, ghrelin, insulin, growth hormone and metabolites in swine
- Parieto-occipital encephalomalacia in neonatal hyperammonemia with ornithine transcarbamylase deficiency : A case report
- Molecular analysis of a presymptomatic case of carnitine palmitoyl transferase I (CPT I) deficiency detected by tandem mass spectrometry newborn screening in Japan
- New Molecular Metals Based on a Tetrathiapentalene Donor with Peripheral Methoxy Groups
- Long-Term Outcome of Living Related Renal Transplantation in a Patient with Short Bowel Syndrome
- Edaravone, a Hydroxyl Radical Scavenger, Ameliorates the Severity of Pulmonary Hypertension in a Porcine Model of Neonatal Sepsis
- Determination of 3-hydroxyisovalerylcarnitine and other acylcarnitine levels using liquid chromatography-tandem mass spectrometry in serum and urine of a patient with multiple carboxylase deficiency
- Chemiluminescent Enzyme Immunoassay for Measuring Leptin
- Nucleoside Analogue Therapy Following One-Year Course of Hepatitis B Immunoglobulin in Preventing Hepatitis B Virus Reactivation after Living Donor Liver Transplantation
- The Relationship of Thyroid Cancer with Radiation Exposure from Nuclear Weapon Testing in the Marshall Islands
- Mutation of RET Gene in Chinese Sporadic Medullary Thyroid Carcinoma
- The Nutritional Index 'CONUT' Is Useful for Predicting Long-Term Prognosis of Patients with End-Stage Liver Diseases
- A New Preadipocyte Cell Line, AP-18, Established from Adult Mouse Adipose Tissue
- Mutation and haplotype analyses of the MUT gene in Japanese patients with methylmalonic acidemia
- Conductometric and Volumetric Studies on the Inonization, Hydration, Aggregation, and Coagulation of AOT in Dodecane
- Positive correlations between tumor uptake on FDG PET and energy expenditure of patients with esophageal cancer
- Effects of Polyethylene Glycol on Bovine Intestine Alkaline Phosphatase Activity and Stability
- Extracorporeal Shock Wave Therapy Improves the Walking Ability of Patients With Peripheral Artery Disease and Intermittent Claudication
- Effects of Polyethylene Glycol on Bovine Intestine Alkaline Phosphatase Activity and Stability
- Stabilization of Bovine Intestine Alkaline Phosphatase by Sugars
- Risk factors for pancreatic stone formation in autoimmune pancreatitis over a long-term course
- Mucolipidosis II and III alpha/beta : mutation analysis of 40 Japanese patients showed genotype-phenotype correlation
- Intestinal obstruction caused by colonic metastasis from intrahepatic cholangiocarcinoma 6 years after removal of the primary tumor : report of a case
- Post-transplantation lymphoproliferative disorder in living-donor liver transplantation : a single-center experience
- Cross-sectional study of bone metabolism with nutrition in adult classical phenylketonuric patients diagnosed by neonatal screening
- IS2-05 Children undergoing LRLTx for treatment of Inherited-Metabolic Diseases are prone to higher oxidative stress and complement activity
- Evaluation of valproate effects on acylcarnitine in epileptic children by LC-MS/MS
- Two Siblings with Type 1 Autoimmune Pancreatitis
- Liver Dysfunction and Thrombocytopenia Diagnosed as Intravascular Large B-cell Lymphoma Using a Timely and Accurate Transjugular Liver Biopsy
- Reliability and validity of a new living liver donor quality of life scale
- Retinoid receptors in human esophageal squamous cell carcinoma : Retinoid X receptor as a potent prognostic factor