Amyotrophic Lateral Sclerosis with Demyelinating Neuropathy
スポンサーリンク
概要
- 論文の詳細を見る
Amyotrophic lateral sclerosis (ALS) with demyelinating polyneuropathy is a rare condition. We describe two ALS patients with demyelinating neuropathy. Immunomodulatory therapies brought slight symptomatic benefits to the patients, but the treatments could not halt the progression of ALS. Chance coincidence of the two diseases is unlikely in view of the low prevalence. ALS, mainly consisting of progressive axonal degeneration, might show temporal demyelinating features of peripheral nerves both electrophysiologically and pathologically. The pathomechanism for the demyelination in ALS remains to be elucidated.
著者
-
Suzuki Chieko
Department Of Gastroenterology And Hepatology Yamaguchi University School Of Medicine
-
Mori Fumiaki
Department Of Cardiology Kanto Medical Center Ntt Ec
-
TOMIYAMA Masahiko
Department of Neurological Science, Institute of Brain Science, Hirosaki University School of Medici
-
KIMURA Tamaki
Department of Neurological Science, Institute of Brain Science, Hirosaki University School of Medici
-
Wakabayashi Koichi
Department Of Neuropathology Hirosaki University Graduate School Of Medicine
-
Baba Masayuki
Department Of Neurological Science Hirosaki University School Of Medicine
-
Arai Akira
Department Of Neurological Science Institute Of Brain Science Hirosaki University School Of Medicine
-
MIKI YASUO
Department of Legal Medicine, Kurume University School of Medicine
-
Ueno Tatsuya
Department of Neurology, Aomori Prefectural Central Hospital, Japan
-
Nishijima Haruo
Department of Neurology, Aomori Prefectural Central Hospital, Japan
-
Kon Tomoya
Department of Neurology, Aomori Prefectural Central Hospital, Japan
-
Funamizu Yukihisa
Department of Neurology, Aomori Prefectural Central Hospital, Japan
-
Haga Rie
Department of Neurology, Aomori Prefectural Central Hospital, Japan
-
Kimura Tamaki
Department of Neurology, Aomori Prefectural Central Hospital, Japan
-
Wakabayashi Koichi
Department of Neuropathology, Hirosaki University Graduate School of Medicine, Japan
関連論文
- Suzaku and Multi-Wavelength Observations of OJ 287 during the Periodic Optical Outburst in 2007
- ＜Poster＞15-Deoxy-Δ^12,14-prostaglandin J_2 modifi es profi les of nuclear TDP-43 protein through its direct binding : Implication for the pathogenesis of TDP-43 proteinopathy
- Optical and Near-Infrared Photometric Observation during the Superoutburst of the WZ Sge-Type Dwarf Nova, V455 Andromedae
- ＜Symposium III＞Nubopathies : NUB1-related neurodegenerative diseases
- All-trans-retinoic acid (atRA) increases host resistance to Listeria monocytogenes infection
- Retinoic acid-inducible gene-I（ RIG-I） and diseases
- Glycogen synthase kinase-3β phosphorylates synphilin-1 in vitro
- Thymus-Related Liposarcoma : Report of a Case and Review of the Literature
- FRS-112 Influence of the Early Ticlopidine Discontinuation on Clinical Outcomes following Sirolimmus-Eluting Stent Implantation(FRS23,Clinical Evidence of DES Era (1) (IHD),Featured Research Session (English),The 73rd Annual Scientific Meeting of The Japa
- 2 Prognostic Factors in Patients with Coronary Artery Disease Treated with Sirolimus-eluting Stent : The HIJ-DES registry(Current Status and Future Perspective of Drug-Eluting Stents,Plenary Session 1 (PL-1) (A),The 73rd Annual Scientific Meeting of The J
- PJ-823 The evaluation of angiographic restenotic pattern after sirolimus-eluting stents implantation in patients on hemodialysis : From the HIJC DES Registry(Coronary revascularization, PCI(26)(IHD),Poster Session(Japanese),The 72nd Annual Scientific Meet
- Effect of a late evening snack on the blood glucose level and energy metabolism in patients with liver cirrhosis
- Prolyl 4-hydroxylase inhibitor is more effective for the inhibition of proliferation than for inhibition of collagen synthesis of rat hepatic stellate cells
- HBV-related fulminant hepatic failure : successful intensive medical therapy in a candidate for liver transplantation
- Characteristics of the cell proliferation profile of activated rat hepatic stellate cells in vitro in contrast to their fibrogenesis activity
- Interferon γ- but not α-treatment prevents fibrosis by inhibiting procollagen and tissue inhibitor of metalloproteinase-1 gene expression in pig serum-induced rat liver fibrosis in vivo
- Fulminant hepatitis complicated by small intestine infection and massive hemorrhage
- PE-048 Insulin Treatments Overweigh the Beneficial Effect of Sirolimus Eluting Stent(PE008,Coronary Revascularization, PCI (DES) 1 (IHD),Poster Session (English),The 73rd Annual Scientific Meeting of The Japanese Circulation Society)
- PJ-761 Glycated Hemoglobin and Risk of Cardiovascular Events in Patients without Diabetes in the Heart Institute of Japan Acute Myocardial Infarction(Acute myocardial infarction, clinical(diagnosis / treatment)(12)(IHD),Poster Session(Japanese),The 72nd A
- PJ-650 Predictors of Restenosis in the Patients with Hemodialysis who Underwent Coronary Intervention with Sirolimus Eluting Stents(Coronary revascularization, PCI(23)(IHD),Poster Session(Japanese),The 72nd Annual Scientific Meeting of the Japanese Circul
- Upregulation of α-synuclein by lipopolysaccharide and interleukin-1 in human macrophages
- Discovery of Multiple High-Velocity Narrow Circumstellar Na I D Lines in Nova V1280 Sco
- Optical and Near-Infrared Photometry of Nova V2362 Cyg : Rebrightening Event and Dust Formation
- Anti-Correlation of Near-Infrared and X-Ray Variations of the Microquasar GRS 1915+105 in the Soft State
- Detection of Polarimetric Variations Associated with the Shortest Time-Scale Variability in S5 0716+714
- The 2006 November Outburst of EG Aquarii : the SU UMa Nature Revealed
- Discovery of a WZ Sge-Type Dwarf Nova, SDSS J102146.44+234926.3 : Unprecedented Infrared Activity during a Rebrightening Phase
- NS-4 Epileptic seizure in mice deficient in μ3B subunit of AP-3B complex
- PE-187 Time from aortic valve closure to E_ : A New Index to Quantitatively Assess the Regional Myocardial Ischemia by 2D-Tracking Echocardiography(Echo/Doppler(06)(I),Poster Session(English),The 72nd Annual Scientific Meeting of the Japanese Circulat
- Co-localization of β-peptide and phosphorylated tau in astrocytes in a patient with corticobasal degeneration
- Pathological heterogeneity in progressive supranuclear palsy and corticobasal degeneration
- Hypoglycemic encephalopathy with extensive lesions in the cerebral white matter
- Oligodendrocytes within astrocytes ("emperipolesis") in the cerebral white matter in hepatic and hypoglycemic encephalopathy
- Disseminated intraparenchymal microgranulomas in the brainstem in central nervous system sarcoidosis
- Peculiar venous lesions in fatal hyponatremic brain edema
- Hydranencephaly with extensive periventricular necrosis and numerous ectopic glioneuronal nests
- Multinucleated astrocytes in old demyelinated plaques in a patient with multiple sclerosis
- Retinoic acid-inducible gene-I mediates RANTES/CCL5 expression in U373MG human astrocytoma cells stimulated with double-stranded RNA
- Listeria monocytogenes Induces the Expression of Retinoic Acid-Inducible Gene-I
- The Lewy body in Parkinson's disease : Molecules implicated in the formation and degradation of α-synuclein aggregates
- The role of NEDD8 Ultimate Buster 1, NUB1, in neurodegenerative α-synucleinopathies
- Thiophene, a sulfur-containing heterocyclic hydrocarbon, causes widespread neuronal degeneration in rats
- Hypertrophy of medial globus pallidus and substantia nigra reticulata in 6-hydroxydopamine-lesioned rats treated with L-DOPA : Implication for L-DOPA-induced dyskinesia in Parkinson's disease
- Detection of hepatitis B virus DNA in liver by polymerase chain reaction for the diagnosis of fulminant hepatitis B
- Dwarf Novae in the Shortest Orbital Period Regime. I A New Short Superhump Period Dwarf Nova, OT J055717+683226
- IS090 Persistent Infection of Helicobacter Pylori Is Associated With Impaired Endothelium-dependent Vasomotor Function in Angiographically Normal Coronary Arteries
- ＜Poster＞Cystatin C immunoreactivity and neuronal degeneration in amyotrophic lateral sclerosis
- ＜Symposium III＞Pathology of neuro-glial α-synucleinopathy (Lewy body disease and multiple system atrophy)
- Thalamic retrograde degeneration in the congenitally hydrocephalic rat is attributable to apoptotic cell death
- Convulsive effects of thiophene, a heterocyclic hydrocarbon:Behavioral, electrographic and c-Fos immunocytochemical studies
- Widespread calcium deposits, as detected using the alizarin red S technique, in the nervous system of rats treated with dimethyl mercury
- Measurement of Phosphatidylcholine Hydroperoxide in Mild Ischemia-Reperfusion Injury in Rat Intestine
- PE-295 Bleeding Complications Associated with Dual Antiplatelet Therapy Plus Anticoagulant in Patients who Underwent Percutaneous Coronary Intervention with Drug-Eluting Stents(Coronary revascularization,PCI(11)(IHD),Poster Session(English),The 72nd Annua
- OJ-019 Results of Re-Percutaneous Coronary Intervention to the In-Stent Restenosis of Drug-Eluting Stent in Patients with Hemodialysis(Coronary revascularizaion, PCI(06)(IHD),Oral Presentation(Japanese),The 72nd Annual Scientific Meeting of the Japanese C
- Alpha-fetoprotein-producing lung carcinoma : Report of three cases
- Improvement of Left Ventricular Function by Permanent Direct His-Bundle Pacing in a Case with Dilated Cardiomyopathy
- Frequency of Heparin-lnduced Thrombocytopenia (HIT) and Thrombosis Complications in Patients with Acute Coronary Syndrome
- Endobronchial Neurogenic Tumors Treated by Transbronchial Electrical Snaring and Nd-YAG Laser Abrasion : Report of Three Cases
- Degeneration of spinal dorsal root ganglia in adult rats treated with methylmercury: Chronological observations on the cell bodies, centrally directed axons and presynaptic terminals
- Coexistence of Creutzfeldt-Jakob disease and senile dementia of the Alzheimer type
- Impact of anticoagulant therapy with dual antiplatelet therapy on prognosis after treatment with drug-eluting coronary stents
- Double Primary Lung Carcinoma Consisting of Large Cell Neuroendocrine Carcinoma and Squamous Cell Carcinoma : Report of a Case
- A serotonin 5-HT_ receptor agonist prevents behavioral sensitization to L-DOPA in a rodent model of Parkinson's disease
- The Statistical Mechanical Aspect of H-Theorem
- Small Solitary Pulmonary Metastasis Detected Before Primary Sigmoid Colon Cancer : Report of a Case
- PATHOLOGIAL ANALYSIS ON CORRELATION BETWEEN NUCLEARINCLUSION FORMATION IN THE FEATHER-FOLLICLE EPITHELIUM AND INCIDENCE OF MAREK'S DISEASE : STUDY OF FIELD FLOCKS
- Anal Function During Pregnancy and Postpartum After Ileal Pouch Anal Anastomosis for Ulcerative Colitis
- Spinal cord involvement of primary central nervous system lymphomas : Histopathological examination of 14 autopsy cases
- Miliary brain metastasis presenting with dementia : Progression pattern of cancer metastases in the cerebral cortex
- Case report of an obturator hernia diagnosed by an orthopedist
- Zero-Modes and Physical States in Topological 2-Form Gravity
- An Unusual Case of Chronic Relapsing Tetanus Associated with Mandibular Osteomyelitis
- Diabetic Amyotrophy or Proximal Diabetic Neuropathy an Immune-mediated Condition?
- Hyperesthesia : An Early Manifestation of Diabetic Polyneuropathy
- Effects of Benserazide on L-DOPA-Derived Extracellular Dopamine Levels and Aromatic L-Amino Acid Decarboxylase Activity in the Striatum of 6-Hydroxydopamine-Lesioned Rats
- Similarities and differences among progressive aupranuclear palsy, corticobasal degeneration and Pick's disease
- The cellular pathology of Parkinson's disease
- Sporadic amyotrophic lateral sclerosis with pallido-nigro-luysian degeneration : A TDP-43 immunohistochemical study
- Depression and Outcomes in Hospitalized Japanese Patients With Cardiovascular Disease : Prospective Single-Center Observational Study
- Cellular pathology in multiple system atrophy
- Amyotrophic Lateral Sclerosis with Demyelinating Neuropathy
- A Small Trinucleotide Expansion in the TBP Gene Gives Rise to a Sporadic Case of SCA17 with Abnormal Putaminal Findings on MRI
- Analysis of interaction of Sendai virus V protein and melanoma differentiation-associated gene 5
- Radicular Myoclonus in a Patient with Guillain-Barré Syndrome
- Formation and Degradation of Microscopic Globular Body : A Proteinaceous Spheron Originated from Dendrite [Innovation in Transplant and Regenerative Medicine. The 13th Meeting of Hirosaki International Forum of Medical Science. Communication Center of Hir
- Anatomical Variations of the Extrahepatic Ducts in Dogs: Knowledge for Surgical Procedures
- Lipodystrophy Caused by Repetitive Pegylated Interferon Injection