上顎洞に発生した横紋筋肉腫の1例

概要

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Rhabdomyosarcoma is an extremely rare malignant tumor but in the head and neck region, it is one of the most common malignancies of the mesenchymal tissue. A case of a 18-year-old male with embryonal rhabdomyosarcoma of the left maxillary sinus is presented. He was referred to our clinic because of the left nasal obstruction and gum swelling.<BR>A final histopathological diagnosis was established by several staining methods including H & E, PTAH, Azan-Mallory and silver stains, by immunohistochemical examination with antimyoglobin and anti-actin antibodies, and by electronmicroscopy. In the absence of cross striations this case was diagnosed to have an undifferentiated type of embryonal rhabdomyosarcoma. Whole left maxillectomy including removal of the eye ball and orbit was performed. Postoperatively, the patient recieved 55 Grays by Linac irradiation and VAC therapy (VCR, AMD, CPM) as a chemotherapy. He has been well for 18 months and there has been no evidence of local recuerrence or metastatic disease.