著明な側副血行を示した乳児肝血管腫の1例

概要

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A female infant was hospitalized at 49 days of age, with congestive heart failure and hepatomegaly. A diagnosis of congenital heart disease was made, and the patient was treated with digoxin and diuretics. At 61 days of age, cardiac catheterization and angiography were performed. These studies revealed a large multiple angiomatous lesins in the bilateral lobes of the liver with variant blood supply and massive intrahepatic shunt. The supplying arteries included the right internal thoracic, common hepatic, right inferior phrenic, and left internal thoracic arteries. The right internal thoracic artery was the main supplying artery. Ligation of the bilateral internal thoracic arteries and prednisonc therapy provided a a dramatic improvement in the patient's condition. Prednisonc therapy was discontinued two weeks after the initiation. At present, 9 months after cessation of therapy, the liver is in normal size. The abdominal aortography revealed normal hepatic artery and complete disappearance of the angiomatous lesions.
日本小児外科学会の論文
1980-10-20