Fatal Pulmonary Hypertension in a Patient with Mixed Connective Tissue Disease: Report of an Autopsy Case.
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概要
- 論文の詳細を見る
A 34-yr-old woman with mixed connective tissue disease (MCTD) who died of heart failure due to pulmonary hypertension (PH) is reported. She showed various symptoms and signs over the previous 8 yr, including lymphadenopathy, Raynaud's phenomenon, polyarthralgia, sclerodactylia, esophageal disturbance, PH, Sjören's syndrome and renal tubular acidosis. Autopsy findings revealed severe intimal proliferation with marked luminal narrowing of the small arteries in the lung. Echocardiographic and mechanocardiographic methods were very useful for assessment of the degree of right ventricular dysfunction associated with PH on the early stage of MCTD.(Internal Medicine 31 : 74-77, 1992)
- 社団法人 日本内科学会の論文
著者
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Hiwada Kunio
The Second Department Of Internal Medicine Ehime University School Of Medicine
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Shigematsu Yuji
The Second Department of Internal Medicine, Ehime University School of Medicine
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Sekiya Michihito
The Second Department of Internal Medicine, Ehime University School of Medicine
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Suzuki Makoto
The Second Department of Internal Medicine, Ehime University School of Medicine
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Hamada Mareomi
The Second Department Of Internal Medicine Ehime University School Of Medicine
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GO Soei
Ehime College of Science and Health
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