Congenital Ocular Motor Apraxia (Cogan)-Report of Two Cases-

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In 1952, Cogan described an unusual clinical condition in four pediatric cases under the name of "congenital ocular motor apraxia".<BR>The first Japanese case of this condition was reported by Inatomi in 1960. The authors preesented two male infants afflicted with conditions closely similar to those described by Cogan, and compared them with 34 cases which were collected from the literature.<BR>The first case, aged two years seven months boy, had shown abnormal side to side head shaking movement associated with peculiar eye movement since 5 or 6 months of age. We found out the cerebral juxtabasal telangiectasia in verte bral angiography, but no other clinical manifes tations except the ocular apraxia.<BR>The second case, aged six months old boy, had shown the similar head and eye movements since 2 months of age. His grandfathers were brother. No accidents were noticed in intrauterine period but he had affected with cerebral palsy (variable rigid quadriplegia, moderate degree, unknown etiology) complicated with bilateral congenital blepharoptosis, high arched palate and umbilical hernia. We found out the asymmetric (lt>rt) enlargement of lateral ventricle (Evans ratio=0.32) and cortical atrophy on P.E.G.
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