Rapid Progression of Neuromuscular Disorder Related Cardiomyopathy in a Young Patient
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概要
- 論文の詳細を見る
An 11-year and 3-month-old boy with a neuromuscular disorder was admitted for dyspnea. Echocardiography revealed severe left ventricular dysfunction with an ejection fraction (EF) of 17%. However, the EF had been 57% when the patient was 10 years and 9 months old. The patient's clinical condition became refractory, and he died on the 155th day of hospitalization. Speckle-tracking analysis was retrospectively performed, which demonstrated that the global radial strain was within the normal range; however, the global longitudinal and circumferential strains were lower -than -normal 10 years and 9 months of age. Adult neuromuscular disorder-related secondary cardiomyopathy generally progresses slowly, although progression depends on the age of onset of cardiomyopathy.
- 社団法人 日本内科学会の論文
著者
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Hayashi Mayuko
Department Of Hematology Meitetsu Hospital
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Kawano Seiji
Department Of Clinical Laboratory Kobe University Hospital
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Awano Hiroyuki
Department Of Pediatrics Graduate School Of Medicine Kobe University
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YAGI Mariko
Department of Clinical Evaluation of Pharmacotherapy, Kobe University Graduate School of Medicine
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Hirata Ken-ichi
Division Of Cardiovascular Medicine Department Of Internal Medicine Kobe University Graduate School
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Kawai Hiroya
Division Of Cardiovascular And Respiratory Medicine Department Of Internal Medicine Kobe University
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Yamamoto Tetsushi
Department Of Chemistry Faculty Of Engineering Gifu University
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Tanaka Hidekazu
Division Of Bio-system Pharmacology Department Of Pharmacology Graduate School Of Medicine Osaka Uni
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Hayashi Nobuhide
Department Of Clinical Laboratory Kobe University Hospital
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Takeshima Yasuhiro
Department of Pediatrics, Kobe University Graduate School of Medicine, Japan
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TAKESHIMA Yasuhiro
Department of Neurosurgery, Nara Medical University
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Lee Tomoko
Department of Pediatrics, Kobe University Graduate School of Medicine, Japan
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Imanishi Takamitsu
Department of Clinical Laboratory, Kobe University Hospital, Japan
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Yamamoto Tetsushi
Department of Clinical Laboratory, Kobe University Hospital, Japan
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Awano Hiroyuki
Department of Pediatrics, Kobe University Graduate School of Medicine, Japan
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