骨 Paget 病による難聴について

概要

論文の詳細を見る
A case of mixed-type hearing impairment due to Paget's disease of bone found in a Japanese woman was reported. A 29 year-old-female, who had had bilateral hearing impairment since her childhood, visited us because of aggravation of hearing loss. The right eardrum was intact, but the handle of the malleus looked thin. The left eardrum showed a dry perforation which presumably resulted from previous surgery at the age of 16. Audiometry revealed mixed-type hearing impairment of about 85dB on the average with reduced bone conduction of about 35dB in both ears.In both ears surgery revealed interruption of the ossicular chains due to absorption of the ossicles. All the ossicles were thin, and there was complete loss of the stapes including its footplate. The horizontal portion of the bony facial canal was thick, causing narrowing of the vestibular window. In contrast, the bone was thin over the cochlear wall around the vestibular and cochlear windows. The bony trabecullae of the mastoid air cells were also unusually thin. However, reconstruction of the ossicular chain in the right ear resulted in moderate improvement of hearing in the lower frequencies, which was not sufficient to allow her to dispense with hearing aids.Although Paget's disease has been very rare in Japan, the number of reported cases has increased recently. This is the second report in the Japanese otolaryngological literature which describes hearing impairment associated with Paget's disease of the bone. The authors point out that Paget's disease should be included in the differential diagnosis of hearing impairment even in Japan.
耳鼻咽喉科臨床学会の論文

骨 Paget 病による難聴について

スポンサーリンク

概要

著者

関連論文

スポンサーリンク