A case of incontinentia pigmenti.

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A case is presented of a little girl with incontinentia pigmenti. The patient had seen a dermatologist soon after birth because of erythematous eruption of the whole body. At 7 days old, desquamation occured on extremities, body and face. At 14 days old, pigmentation occured on same lesion of the eruption. A panoramic film showed, at age of two, eight missing milk teeth and shortage of permanent teeth and deformity of some teeth. General condition was good and physical features were medium. But vertical hair was falling out within 2.7cm×1.2cm area, and on trunk and legs and arms, pigmentation were observed. At 4 years of age, she had denture put in, and problems of beauty and function of occulusion were solved. Now the patent is 5 years old, the pigmentation is still existent and no resuscitation is shown of the vertical hair. Denture is now stabilized.