Myelofibrosis Successfully Treated with Prednisolone in a Patient with Pachydermoperiostosis
スポンサーリンク
概要
- 論文の詳細を見る
Pachydermoperiostosis (PDP) is a rare disorder of bone and connective tissue growth. A 21-year-old man was referred to our hospital with anemia. He showed characteristics of PDP. Bone marrow biopsy showed myelofibrosis. Chromosomal abnormalities or JAK2 mutation were not found. Anemia gradually progressed, and he became transfusion-dependent. Oral prednisolone was initiated; it gradually improved his anemia and rendered the patient free of transfusion. However, other clinical symptoms such as clubbed fingers and skin hypertrophy remained unimproved. In this case, the serum concentration of vascular endothelial growth factor and transforming growth factor-β levels were increased. Further investigation will be necessary to establish appropriate treatment strategies for this disease.
著者
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Ogawa Yoko
Department Of Cardiovascular Medicine The University Of Tokyo
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Moriwaki Hisataka
The First Department Of Internal Medicine Gifu University School Of Medicine
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Seishima Mariko
Department Of Dermatology Gifu University Graduate School Of Medicine
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Hirose Yoshinobu
Department Of Clinical Pathology Gifu University Hospital
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Kasahara Senji
The First Department of Internal Medicine, Graduate School of Medicine, Gifu University, Japan
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Tsurumi Hisashi
The First Department of Internal Medicine, Graduate School of Medicine, Gifu University, Japan
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Ogawa Yoko
Department of Dermatology, Gifu University Graduate School of Medicine, Japan
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Ninomiya Soranobu
The First Department of Internal Medicine, Gifu University Graduate School of Medicine, Japan
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Hara Takeshi
The First Department of Internal Medicine, Gifu University Graduate School of Medicine, Japan
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Kanemura Nobuhiro
The First Department of Internal Medicine, Gifu University Graduate School of Medicine, Japan
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Tsurumi Hisashi
The First Department of Internal Medicine, Gifu University Graduate School of Medicine
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Tsurumi Hisashi
The First Department of Internal Medicine, Gifu University Graduate School of Medicine, Japan
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Kasahara Senji
The First Department of Internal Medicine, Gifu University Graduate School of Medicine
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Kasahara Senji
The First Department of Internal Medicine, Gifu University Graduate School of Medicine, Japan
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Seishima Mariko
Department of Dermatology, Gifu University Graduate School of Medicine, Japan
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Hirose Yoshinobu
Department of Tumor Pathology, Gifu University Graduate School of Medicine, Japan
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