Type II Citrullinemia in an Elderly Patient Treated with Living Related Partial Liver Transplantation
スポンサーリンク
概要
- 論文の詳細を見る
A 60-year-old woman was admitted to our hospital for repeated consciousness disturbance. Blood examination showed hyperammonemia, and plasma amino acid analysis revealed a marked increase in the citrulline level. To establish a diagnosis, a percutaneous needle biopsy of the liver was performed. The determination of the urea cycle enzyme activities revealed a selective marked decrease in argininosuccinate synthetase activity, indicating the final diagnosis of type II citrullinemia. The mean survival period of this disease after the appearance of symptoms has been reported as 26.4 months, and most conservative treatments are not effective. We performed a living related partial liver transplantation. Over the subsequent 13-month follow-up, the patients condition has remained fairly good.(Internal Medicine 39: 553-558, 2000)
- 社団法人 日本内科学会の論文
著者
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MORIWAKI H.
Gifu University School of Medicine
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Moriwaki Hisataka
岐阜大学 医学部内科学
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Moriwaki Hisataka
がん･感染症センター都立駒込病院 肝臓内科
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OHNISHI Hiroo
First Department of Internal Medicine Gifu University School of Medicine
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Moriwaki Hisataka
The First Department Of Internal Medicine Gifu University School Of Medicine
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Yasuda Ichiro
First Department Of Internal Medicine Gifu University Hospital
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Yasuda I
Univ. Tokyo Tokyo Jpn
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Yasuda I
Gifu Univ. School Of Medicine Gifu Jpn
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Yasuda Ichiro
Department Of Earth And Plantary Science Graduate School Of Science University Of Tokyo
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YAMAKITA Noriyoshi
Matsunami General Hospital
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Matsunami Hidetoshi
Matsunami General Hospital
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Ohnishi Hiroo
The First Department Of Internal Medicine Gifu University School Of Medicine
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Yasuda Ichiro
The First Department Of Internal Medicine Gifu University School Of Medicine
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Moriwaki H
Gifu Univ. School Of Medicine Gifu Jpn
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TAKENAKA Kiyoyuki
the First Department of Internal Medicine, Gifu University School of Medicine
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ARAKI Hiroshi
the First Department of Internal Medicine, Gifu University School of Medicine
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NAITO Tomoo
the First Department of Internal Medicine, Gifu University School of Medicine
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FUKUTOMI Yasushi
the First Department of Internal Medicine, Gifu University School of Medicine
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HASEGAWA Takeshi
Matsunami General Hospital
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SATO Hirohide
Matsunami General Hospital
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SHIMIZU Yasunobu
Matsunami General Hospital
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Fukutomi Yasushi
The First Department Of Internal Medicine Gifu University School Of Medicine
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Naito Tomoo
The First Department Of Internal Medicine Gifu University School Of Medicine
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Ohnishi Hiroo
Department Of Internal Medicine Gifu University School Of Medicine
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Takenaka Kiyoyuki
The First Department Of Internal Medicine Gifu University School Of Medicine
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Araki Hiroshi
The First Department Of Internal Medicine Gifu University School Of Medicine
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