Durable Hypogammaglobulinemia Associated with Thymoma (Good Syndrome)
スポンサーリンク
概要
- 論文の詳細を見る
Good syndrome, characterized by hypogammaglobulinemia and acquired immunodeficiency, is a rare condition associated with thymoma. A 67-year-old woman, who 4 months previously had a thymoma resected, presented with generalized hypogammaglobulinemia with a severely decreased B cell population as demonstrated by flow cytometry. She was diagnosed as having bacterial mediastinitis associated with Good syndrome. For the subsequent 6 years, she suffered from repeated serious bacterial infections. As this paraneoplastic syndrome is not resolved by tumor removal, careful management with intensive infection-control using antibiotics and intravenous immunoglobulins is required for the long term. Serum immunoglobulin levels should be evaluated for patients with thymoma and suspected vulnerability to infection.
- 社団法人 日本内科学会の論文
著者
-
Tochigi Naobumi
Pathology Division National Cancer Center Research Institute
-
Watanabe Shun-ichi
Thoracic Surgery Division National Cancer Center Hospital
-
Tanabe Nobuhiro
Department Of Chemistry Faculty Of Science Kyoto University
-
Kurosu Katsushi
Department Of Respirology (b2) Graduate School Of Medicine Chiba University
-
Tatsumi Koichiro
Department Of Chest Medicine School Of Medicine Chiba University
-
Takiguchi Yuichi
Department Of Chemotherapy Graduate School Of Medicine Chiba University
-
Kitamura Atsushi
Department Of Respirology Graduate School Of Medicine Chiba University
-
Sakao Seiichirou
Department of Respirology, Graduate School of Medicine, Chiba University
-
Tochigi Naobumi
Pathology Division, National Cancer Center, Research Institute
関連論文
- A New Aspect of the Carotid Body Function Controlling Hypoxic Ventilatory Decline in Humans
- A Case of Isolated Peripheral Pulmonary Artery Branch Stenosis Associated with Multiple Pulmonary Artery Aneurysms
- Epidermal growth factor receptor mutation status and clinicopathological features of combined small cell carcinoma with adenocarcinoma of the lung
- Effects of Long-Acting Beraprost Sodium (TRK-100STP) in Japanese Patients With Pulmonary Arterial Hypertension
- Multidetector-Row Computed Tomography Management of Acute Pulmonary Embolism
- Basaloid squamous-cell carcinoma of the lung in a young woman
- Dose evaluation and effective dose estimation from CT fluoroscopy-guided lung biopsy
- Clinical Characteristics, Diagnosis and Management of Patients With Pulmonary Thromboembolism Who are Not Diagnosed in the Acute Phase and Not Classified as Chronic Thromboembolic Pulmonary Hypertension
- Inferior Vena Cava Filter is a New Additional Therapeutic Option to Reduce Mortality From Acute Pulmonary Embolism
- Gender Differences in Chronic Thromboembolic Pulmonary Hypertension in Japan
- Dilatation of Bronchial Arteries Correlates With Extent of Central Disease in Patients With Chronic Thromboembolic Pulmonary Hypertension
- Survival and Quality of Life for Patients With Peripheral Type Chronic Thromboembolic Pulmonary Hypertension
- Spontaneous Disappearance of a Pulmonary Lesion in a Patient with Active Wegener's Granulomatosis
- Decreased Lipoprotein Lipase in Obstructive Sleep Apnea Syndrome
- Angiotensin-Converting Enzyme Gene Polymorphisms and Prognosis in Chronic Thromboembolic Pulmonary Hypertension
- Vascular Endothelial Growth Factor in Obstructive Sleep Apnea Syndrome
- Phase I study of cisplatin and irinotecan combined with concurrent hyperfractionated accelerated thoracic radiotherapy for locally advanced non-small cell lung carcinoma
- Continuous Positive Airway Pressure Therapy and Tracheostomy for Multiple System Atrophy Accompanied by Sleep Apnea-hypopnea Syndrome
- Placement of Metallic Stents for Critical Airway Stenosis Due to Malignant Diseases
- Thermoradiotherapy for local control of chest wall invasion in patients with advanced non-small cell lung cancer
- OE-227 Right Atrium Contractility and Right Ventricular Diastolic Function Assessed by Pulsed-Tissue-Doppler-Imaging Can Predict Brain-Natriuretic-Peptide in Adults with Acquired Pulmonary Hypertension(Pulmonary circulation(01)(H),Oral Presentation(Englis
- An Efficient Synthesis of Linear Porphyrin Arrays
- Estimation of Elevated Brain Natriuretic Peptides by Pulsed Doppler Tissue Imaging in Patients with Pulmonary Hypertension(Pulmonary Circulation 1 (H), The 69th Annual Scientific Meeting of the Japanese Circulation Society)
- Successful Resection of Hepatocellular Carcinoma with Bronchobiliary Fistula Caused by Repeated Transcatheter Arterial Embolizations : Report of a Case
- A Case of Pulmonary Artery Bypass Surgery for a Patient with Isolated Takayasu Pulmonary Arteritis and a Review of the Literature
- Characteristics of Acute Pulmonary Thromboembolism in Patients Hospitalized for Medical Illness : Results of a Multicenter Registry in JaSPER (Pulmonary Circulation 4 (H), The 69th Annual Scientific Meeting of the Japanese Circulation Society)
- Lymphangioleiomyomatosis with a Giant Bulla : Report of a Case
- In vitro conversion of irinotecan to SN-38 in human plasma
- Arterial and Mixed Venous Oxygen Desaturation during Incremental Exercise in Patients with Chronic Pulmonary Disease
- Inhibitory mechanisms in hypoxic respiratory depression studied in an in vitro preparation
- Control of Upper Airway Function in Response to Hypoxia in Patients with Obstructive Sleep Apnea Syndrome
- Compensatory Excretion of Prostacyclin and Thromboxane Metabolites in Obstructive Sleep Apnea Syndrome
- Efficacy of Perioperative Administration of Long-Acting Bronchodilator on Postoperative Pulmonary Function and Quality of Life in Lung Cancer Patients with Chronic Obstructive Pulmonary Disease. Preliminary Results of a Randomized Control Study
- A phase III, multicenter, collaborative, open-label clinical trial of sildenafil in Japanese patients with pulmonary arterial hypertension
- A Convenient Synthesis of Polyyne-bridged Porphyrin Dimers
- Risk of Acute Exacerbation of Interstitial Pneumonia After Pulmonary Resection for Lung Cancer in Patients with Idiopathic Pulmonary Fibrosis Based on Preoperative High-Resolution Computed Tomography
- Effects of obstructive sleep apnea syndrome on hepatic steatosis and nonalcoholic steatohepatitis
- Synergistic effect of non-transmissible Sendai virus vector encoding the c-myc suppressor FUSE-binding protein-interacting repressor plus cisplatin in the treatment of malignant pleural mesothelioma
- Juvenile Pulmonary Hypertension Associated with Fibromuscular Dysplasia
- Early Detection of COPD in Patients with Dyspnea on Exertion in General Practice
- Immunogenicity of a monovalent pandemic influenza A H1N1 vaccine in health-care workers of a university hospital in Japan
- Serum Level of Fibrinogen Aα Chain Fragment Increases in Chronic Thromboembolic Pulmonary Hypertension
- An early event of EGFR mutation in pleomorphic carcinoma of the lung
- HLA-DPB1 and NFKBIL1 may confer the susceptibility to chronic thromboembolic pulmonary hypertension in the absence of deep vein thrombosis
- Improved Survival in Medically Treated Chronic Thromboembolic Pulmonary Hypertension
- Double-Blind, Placebo-Controlled Clinical Trial With a Rho-Kinase Inhibitor in Pulmonary Arterial Hypertension:– A Pilot Efficacy Trial –
- Spontaneously Remitted Pulmonary Arterial Hypertension Associated with the Herbal Medicine "Bofutsushosan"
- Metastatic Gastric Cancer from Squamous Cell Lung Carcinoma
- Pulmonary Toxicity by an Oral Anti-neoplastic Agent, S-1
- Usefulness of Low-dose Methotrexate Monotherapy for Treating Sarcoidosis
- Current Venous Thromboembolism Management and Outcomes in Japan:– Nationwide The Japan Venous Thromboembolism Treatment Registry Observational Study –
- Survival of Japanese Patients with Pulmonary Arterial Hypertension after the Introduction of Endothelin Receptor Antagonists and/or Phosphodiesterase Type-5 Inhibitors
- Durable Hypogammaglobulinemia Associated with Thymoma (Good Syndrome)
- Clinical Classification of Targeted Agents Used for Anticancer Treatment
- Double-Blind, Placebo-Controlled Clinical Trial With a Rho-Kinase Inhibitor in Pulmonary Arterial Hypertension : A Pilot Efficacay Trial
- Improved Survival in Medically Treated Chronic Thromboembolic Pulmonary Hypertension
- Long-term Survival of Japanese Patients with Pulmonary Arterial Hypertension Treated with Beraprost Sodium, an Oral Prostacyclin Analogue