Budd-Chiari Syndrome Associated with Hypereosinophilic Syndrome; A Case Report
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概要
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A 27-year-old man was admitted due to abdominal fullness. He had ascites and subcutaneous nodules on his head, with liver dysfunction and eosinophilia. Abdominal imaging revealed obstruction of the hepatic veins and stenosis of the inferior vena cava. Histological diagnosis of a subcutaneous nodule revealed obstructive thrombophlebitis with eosinophils. Tyrosine kinase created by fusion of the FIP1L1 and PDGFRA genes, which is characteristic of hypereosinophilic syndrome (HES), was detected. He was diagnosed with Budd-Chiari syndrome associated with HES. Liver function tests improved after interventional therapy followed by steroid therapy. It is important to diagnose the cause of Budd-Chiari syndrome.
著者
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Matsui Hidetaka
Department Of Gastroenterology And Metabology Ehime University Graduate School Of Medicine
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Matsuura Bunzo
Department Of Gastroenterology And Metabology Ehime University Graduate School Of Medicine
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Konishi Ichiro
Department Of Gastroenterology And Metabology Ehime University Graduate School Of Medicine
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Horiike Norio
Department Of Gastroenterology And Metabology Ehime University Graduate School Of Medicine
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HIROOKA MASASHI
Department of Gastroenterology and Metabology, Ehime University Graduate School of Medicine
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MIYAOKA HIROAKI
Internal Medicine, Saiseikai Matuyama Hospital
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Shigematsu Shuichiro
Department Of Gastroenterology And Metabology Ehime University Graduate School Of Medicine
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Hiasa Yoichi
Department Of Gastroenterology And Metabology Ehime University Graduate School Of Medicine
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Hato Takaaki
Department Of Bioregulatory Medicine Ehime University Graduate School Of Medicine
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Onji Morikazu
Department Of Gastroenrerology And Metabology Ehime University Graduate School Of Medicine
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Michitaka Kojiro
Department Of Gastroenrerology And Metabology Ehime University Graduate School Of Medicine
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Inoue Ai
Department of Gastroenterology and Metabology, Ehime University Graduate School of Medicine, Toon-city
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Hirooka Masashi
Department of Gastroenterology and Metabiology, Ehime University Graduate School of Medicine, Japan
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Hirooka Masashi
Department of Gastroenterology and Metabology, Ehime University Graduate School of Medicine, Toon-city
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Michitaka Kojiro
Department of Endoscopic Medicine, Ehime University Graduate School of Medicine
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Konishi Ichiro
Department of Gastroenterology and Metabology, Ehime University Graduate School of Medicine, Toon-city
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Hiasa Yoichi
Department of Gastroenterology and Metabiology, Ehime University Graduate School of Medicine, Japan
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Miyaoka Hiroaki
Internal Medicine, Saiseikai Matsuyama Hospital
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Matsuura Bunzo
Department of Gastroenterology and Metabiology, Ehime University Graduate School of Medicine, Japan
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Matsuura Bunzo
Department of Gastroenterology and Metabology, Ehime University Graduate School of Medicine, Toon-city
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