Crow-Fukase syndrome associated with high-output heart failure

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概要

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• A 64-year-old woman was admitted with systemic edema and exertional dyspnea. High-output heart failure was diagnosed by right heart catheterization and she was treated with diuretics. After 3 weeks, her symptoms disappeared but a high cardiac output state persisted. A diagnosis of Crow-Fukase syndrome was made based on the presence of polyneuropathy, organomegaly, endocrinopathy, M-protein, and skin changes. Her serum vascular endothelial growth factor (VEGF) level was markedly elevated after recovery from heart failure. We suspect that an elevated VEGF level and a high cardiac output state may play a role in the pathogenesis of heart failure in Crow-Fukase syndrome.

• The Japanese Society of Internal Medicine = 日本内科学会の論文
• 2002-08-01

著者

• Shimizu Masami

  Molecular Genetics of Cardiovascular Disorders, Division of Cardiovascular Medicine, Graduate School

• Konno Tetsuo

  The Department Of Internal Medicine Saiseikai Kanazawa Hospital

• ARAKI Tsutomu

  The Department of Cardiology, Kanazawa Cardiovascular Hospital

• Takimoto Hiroaki

  The Department Of Internal Medicine Saiseikai Kanazawa Hospital

• SOMA Ryuichiro

  The Department of Internal Medicine, Saiseikai Kanazawa Hospital

• NAKASHIMA Akikatsu

  The Department of Internal Medicine, Saiseikai Kanazawa Hospital

• TOFUKU Yohei

  The Department of Internal Medicine, Saiseikai Kanazawa Hospital

• Nakashima Akikatsu

  The Department Of Internal Medicine Saiseikai Kanazawa Hospital

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