Masculinizing operation for a female patient with congenital adrenocortical hyperplasia due to 21-hydroxylase deficiency

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21・hydroxylase欠損による先天性副腎皮質過形成をもつ25歳女子(戸籍上は男子)症例に対して2度にわたる男性化手術をおこなった.1度目は卵巣子宮附属器切除術と索切除術であり,2度目は11ヵ月後の尿道形成術と両側偽睾丸挿入術である.術後の排尿機能と勃起の状態は良好であった.A 25-year-old female with simple virilizing type of congenital adrenocortical hyperplasia due to 21-hydroxylase deficiency was treated surgically with masculinizing operations which consisted of two-stage procedures. The first procedure was chordectomy associated with excision of both gonads and female internal genitalia. Eleven months later, the second procedure consisting of urethroplasty and implantation of testicular prosthesis was performed. The postoperative course was successful in terms of urination and penile erection.