新生児胃破裂をきたした Megacystis-Microcolon Intestinal-Hypoperistalsis-Syndromeの1例

概要

論文の詳細を見る
A case of megacystis-microcolon-intestinal hypoperistalsis syndrome (MMIHS), complicated with gastric perforation is presented. This was the only case of gastric perforation in 28 MMIHS cases ever reported in the world literature. The etiology of the perforation was thought to be a large defect in the musculature of the stomach, complicated with distal obstruction due to hypoperistalsis. A review of the literature revealed that there have been many common characteristcs; flaccid abdomen, megacystis, malrotation, undescended testis, and so on; descrived in MMIHS and prune belly syndrome (PBS). In view of so much similarity between these two syndromes, we suggest that MMIHS might be a female manifestation and PBS being a male type expression of the same underlying process.
日本小児外科学会の論文
1984-10-20