左右肝管合流部に巨大な単胞性嚢胞状拡張を伴った先天性胆道拡張症の1例

概要

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A case of congenital choledochal dilatation with an unilocular cystic dilatation of the confluence of the right and the left hepatic duct in a 5-years-old boy is reported. The patient was referred to the Ryukyu University Hospital with a possible diagnosis of congenital choledochal cyst with liver cyst. On admission, he appeared essentially normal. US and CT studies demonstrated choledochal cystic dilatation and an unilocular intrahepatic cystic lesion. Scintigrams (^<99m>Tc) revealed that the intrahepatic cystic lesion was cystic dilatation of the intra-hepatic bile duct. At surgery, the choledochus was cystically dilated and intrahepatic cystic lesion bulged out from the hilar hepatic surface. The common hepatic duct appeared normal and mediated between both cystic lesions, just like a bridge acrossing the river. Operative cholangiograms demonstrated that the intrahepatic cystic lesion was an unilocular cystic dilatation of the confluence of the right and the left hepatic duct. The cystically dilated choledochus was resected, and cysto (intrahepatic) -jejunostomy (Roux-Y) was performed. He was been doing well after surgery.
日本小児外科学会の論文
1991-10-20