<症例>多発平滑筋腫を伴なった腟欠損症(Mayer-Rokitansky-Kuster Syndrome)の1例

概要

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Absence of the vagina results from an embryological arrest in the development of the lower portion of the Muellerian ducts. This produces, consequently, not only the absence of the vagina, but also the absence of the uterine fundus and cervix as well, since the uterus is also derived from Muellerian ducts. But the ovaries are normal, since their origin is from quite a different source. In 1961,Hauser advocated that the term of Mayer-Rokitansky-kuster Syndrome, the triad are a) absence of the vagina, b) uterus bicornis rudimentarius solidum, c) normal ovaries. And this syndrome is not infrequently reported, usually in association with urinary tract anomalies. Association with urinary tract anomalies is not hard to understand, when one remembers that in early embryological life the urogenital fold is the anlage of important parts of both the genital and urinary systems. Recently, we had a case of leiomyomata with Mayer-Rokitansky-Kuster Syndrome. As it is generally speaking, uterine fibroid was not found in the non-functioning uterus. Such an anomaly occurring in association with leiomyomata raises the question as to the histogenesis of these tumors.
近畿大学の論文
1976-11-01