後天性C1-INH欠損性血管浮腫例

概要

論文の詳細を見る
Angioedema is a rare disease characterized by mucosal or submucosal swelling. If this occurs in the upper pharynx or larynx, it may become life-threatening and requires emergency treatment. We report a case of angioedema associated with C1-inhibitor (C1-INH) deficiency. A 51-year old woman seen for laryngeal edema and facial and neck swelling, showed no increased number of white blood cells or C-reactive protein. C3, C4, CH50, and C1-INH, functions were markedly decreased, however, indicating hereditary angioedema (HAE) or acquired angioedema (AAE). Additional examination showed decreased C1q, yielding a diagnosis of AAE. Following tranexamic acid administrations no recurrence has been observed to date.
耳鼻咽喉科臨床学会の論文
2010-12-01