Dilated Phase of Hypertrophic Cardiomyopathy Caused by Two Different Sarcomere Mutations, Treated with Surgical Left Ventricular Reconstruction and Cardiac Resynchronization Therapy with a Defibrillator
スポンサーリンク
概要
- 論文の詳細を見る
We herein report the case of a 61-year-old woman with dilated phase of hypertrophic cardiomyopathy (D-HCM) who had been diagnosed with HCM 17 years previously. On admission, her left ventricle (LV) had marked dilation, dyssynchrony with diffuse severe hypokinesis, and ventricular tachycardia. She had two mutations in the cardiac myosin binding protein-C gene, which were suspected to be the causes of the D-HCM. We performed LV reconstruction surgery and cardiac resynchronization therapy with a defibrillator for her drug-resistant severe heart failure. After surgery, her New York Heart Association class dramatically improved, and she has not been re-hospitalized since these treatments.
著者
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SATO Akihiko
Department of Gastroenterology, Tohoku University School of Medicine
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Uekita Hironori
Department Of Cardiology And Hematology Fukushima Medical University
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Kimura Akinori
Department Of Diagnostic And Therapeutic Radiology Ehime University Graduate School Of Medicine
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Ando Katsuya
Department Of Biological Science Faculty Of Science Kanagawa University
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Sakamoto Nobuo
Department of Biomedical Chemistry, School of Medicine, Nagoya University
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Yamaki Takayoshi
Department Of Cardiology And Hematology Fukushima Medical University
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Arimura Takuro
Department Of Molecular Pathogenesis Division Of Adult Diseases
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Suzuki Hitoshi
Department Of Animal Science Faculty Of Agriculture Tohoku University
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SAITOH Shu-ichi
Department of Cardiology and Hematology, Fukushima Medical University
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Takeishi Yasuchika
Department Of Advanced Cardiac Therapeutics Fukushima Medical University
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Nakazato Kazuhiko
Department Of Cardiology And Hematology Fukushima Medical University
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Kunii Hiroyuki
Department Of Cardiology And Hematology Fukushima Medical University
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SUGIMOTO Koichi
Department of Aeronautics and Astronautics, Faculty of Engineering Kyushu University
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Saitoh Shu-ichi
Department of Cardiology and Hematology, Fukushima Medical University, Japan
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Kaneshiro Takashi
Department of Cardiology and Hematology, Fukushima Medical University, Japan
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Sato Masatomo
Medical Corporation Shoseikai Sato Clinic, Japan
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Tamagawa Kazuaki
Fukushima Prefectural Aizu General Hospital, Japan
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TAMAGAWA KAZUAKI
Fukushima Prefectural Aizu General Hospital
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Nakazato Kazuhiko
Department of Cardiology and Hematology, Fukushima Medical University, Japan
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Kaneshiro Takashi
Department of Cardiology and Hematology, Fukushima Medical University
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Uekita Hironori
Department of Cardiology and Hematology, Fukushima Medical University, Japan
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Arimura Takuro
Department of Molecular Pathogenesis, Medical Research Institute, Tokyo Medical and Dental University, Japan
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Yamaki Takayoshi
Department of Cardiology and Hematology, Fukushima Medical University, Japan
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Sugimoto Koichi
Department of Cardiology and Hematology, Fukushima Medical University, Japan
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Kunii Hiroyuki
Department of Cardiology and Hematology, Fukushima Medical University, Japan
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Kimura Akinori
Department of Molecular Pathogenesis, Medical Research Institute, Tokyo Medical and Dental University, Japan
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