A case of Dysostosis cleido-cranialis.

概要

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Cleidocranial dysostosis is a congenital angmaly with clavicle and cranial osteogenesis imperfecta accompanied by abnormality of dental eruption.<BR>This disease was first reported in 1765 by Martin and named cleidodranial dysostosis in 1897 by Sainton and Marie.<BR>In our country it was documented first by Takahashi in 1925. It is a relatively rare disease not only in Japan but also in occidental countries.<BR>Recently we encountered 21-year-old male patient with absence of bilateral clavicle and zygomatic arch fontanel opening, separation of public symphysis, prolonged retention of deciduous teeth, and 23 impacted teeth.<BR>Treatment consisted first of extraction of deciduous teeth and then of fenestration in the regions of the left and right canines and first premolars of the mandible. Resin buttons were attached to these teeth for traction with rubber bands. The patient is at present in a careful follow-up study.
社団法人日本口腔外科学会の論文