術前に診断しえたCruveilhier-Baumgarten病の1症例

概要

論文の詳細を見る
A 51-year-old woman with cholecystolithiasis was transferred to Nagasaki University Hospital for an evaluation of splenomegaly, venous marking on the abdomen, and a small sized morphologically normal liver. Pancytopenia was pointed out by a blood examination. Esophageal varices were demonstrated by an esophagography. Computed tomography, ultrasonography and abdominal angiography revealed splenomegaly, non-cirrhotic small liver and patent umbilical and paraumbilical veins. A percutaneous transhepatic portography (PTP) demonstrated large tortuous umbilical and paraumbilical veins arising from the left portal branch, and then partially bypassed through the bilateral ileac veins into the inferior vena cava. A PTP portal vein pressure increased to 335mmH<SUB>2</SUB>O. According to these findings, preoperative diagnosis of Cruveilhier-Baumgarten disease was established. Laparatomy revealed a small sized, smooth surfaced liver, suggestive of diminished intrahepatic portal circulation and dilatated umbilical and paraumbilical veins. Splenectomy and hepatic periarterial neurectomy were performed on this patient to reduce the augmented portal pressure and to provide an increase of hepatic arterial blood flow. Splenectomy provided to reduce the portal pressure within normal limits. A morphologically normal liver was confirmed by a wedged biopsy of the liver. The postoperative course was uneventful with diminished esophageal varices.
社団法人日本肝臓学会の論文

術前に診断しえたCruveilhier-Baumgarten病の1症例

スポンサーリンク

概要

著者

関連論文

スポンサーリンク