Treatment of a Japanese Patient with Familial Amyloidotic Polyneuropathy with Orthotopic Liver Transplantation.
スポンサーリンク
概要
- 論文の詳細を見る
A 28-year-old male patient with familial amyloidotic polyneuropathy (FAP) underwent a liver transplantation from a heart-beating cadaveric donor in Sweden. He had suffered from the disease for 2.5 years. It took 5.5 hours to carry out the operation without blood transfusion. After the liver transplantation, serum amyloidgenic variant transthyretin (TTR) levels became extremely low and diarrhea stopped after the 7th day. On day 13, the patient was discharged from the hospital and one month after the transplantation, his general condition remained quite good. This is the first case of a Japanese patient with congenital metabolic disorders as well as FAP to receive a liver transplantation from a heart-beating cadaveric donor.(Internal Medicine 33: 730-732, 1994)
- 社団法人 日本内科学会の論文
著者
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YAMASHITA Taro
The First Department of Internal Medicine, Kumamoto University School of Medicine
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Ando Masayuki
The First Department Of Internal Medicine Kumamoto University School Of Medicine
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ANDO Yukio
the First Department of Internal Medicine, Kumamoto University School of Medicine
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Uchino Makoto
The First Department Of Internal Medicine Kumamoto University School Of Medicine
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Tanaka Yoshiya
The First Department Of Internal Medicine School Of Medicine University Of Occupational & Enviro
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NAKAZATO Masamitsu
the Third Department of Internal Medicine, Miyazaki Medical College
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TASHIMA Kazuhiro
the First Department of Internal Medicine, Kumamoto University School of Medicine
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ERICZON Bo-Göran
The Department of Transplantation Surgery, Huddinge Hospital
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DURAJ Frans
The Department of Transplantation Surgery, Huddinge Hospital
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SAKASHITA Naomi
The First Department of Internal Medicine, Kumamoto University School of Medicine
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KIMURA En
The First Department of Internal Medicine, Kumamoto University School of Medicine
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ANDO Eiko
Department of Opthalmology, Kumamoto University School of Medicine
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YONEHARA Toshiro
The First Department of Internal Medicine, Kumamoto University School of Medicine
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NAKAMURA Masaaki
The First Department of Internal Medicine, Kumamoto University School of Medicine
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