Slowly Progressive Distal Muscular Atrophy of the Bilateral upper Limbs (O'Sullivan-McLeod Syndrome) Partially Alleviated by Intravenous Immunoglobulin Therapy
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概要
- 論文の詳細を見る
We report a case of O'Sullivan-McLeod syndrome in a 59-year-old man, who had experienced slowly progressive weakening of both hands since he was 20 years of age. Mild hyperIgEemia and eosinophilia were present. Nerve conduction studies revealed reduced F wave-evoked frequencies for the median and ulnar nerves. Intravenous immunoglobulin (IVIG) at a dose of 400 mg/kg/day was given for 5 days. After IVIG, the muscle weakness of the distal upper extremities improved together with increased F wave-evoked frequencies. These effects lasted for a few months. These observations suggest that immune-mediated neural damage partially contributes to O'Sullivan-McLeod syndrome.
- 社団法人 日本内科学会の論文
著者
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Ohyagi Yasumasa
Department Of Neurology Neurological Institute Graduate School Of Medicine Kyushu University 60
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Kikuchi Hitoshi
Department Of Medicine Ii School Of Medicine Iwate Medical University
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Kira Jun-ichi
Department Of Neurology Graduate School Of Medical Sciences Kyushu University
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Kawano Yuji
Department Of Neurology Neurological Institute Graduate School Of Medical Sciences Kyushu University
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Nagara Yuko
Department Of Hematology Hamanomachi Hospital
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MURAI Hiroyuki
Department of Neurology, Neurological Institute, Graduate School of Medical Sciences, Kyushu University
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Ohyagi Yasumasa
Department of Neurology, Neurological Institute, Graduate School of Medical Sciences, Kyushu University
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Nagara Yuko
Department of Neurology, Neurological Institute, Graduate School of Medical Sciences, Kyushu University
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Kawano Yuji
Department of Neurology, Neurological Institute, Graduate School of Medical Sciences, Kyushu University
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