Vasospastic Angina in Patients With Systemic Triglyceride Storage Disease With Jordans' Anomaly and Cardiomyopathy
スポンサーリンク
概要
- 論文の詳細を見る
Vasospastic angina was demonstrated clinically and angiographically in a 54-year-old patient with systemic triglyceride storage disease and cardiomyopathy. He and his younger sister had been diagnosed in 1985 as having systemic triglyceride storage with Jordans' anomaly. In 1993, he began complaining of rest and effort chest pain in the morning, which was accompanied by ST depression by ECG. Sublingual nitroglycerine was effective for treating this pain. Intracoronary injection of acetylcholine induced severe coronary vasoconstriction in the left anterior descending artery. Left ventricular contraction was diffusely impaired. Deposits of numerous triglyceride droplets and a decrease in the density of myofibrils in cardiocytes were found in the specimens obtained by endomyocardial biopsy. The impaired left ventricular contraction may have been due to the changes in myocardial cells. His sister complained of a similar chest pain that was completely controlled by calcium channel antagonist. Thus, our cases demonstrated vasospastic angina associated with cardiomyopathy secondary to systemic triglyceride storage disease with Jordans' anomaly, though the causal relationship between these conditions remains unclear.
- 社団法人日本循環器学会の論文
- 1996-01-20
著者
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Ando Shin-ichi
Research Institute Of Angiocardiology And Cardiovascular Clinic Faculty Of Medicine Kyushu Universit
-
Ando Shin-ichi
九州大学医学部附属心臓血管研究施設
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Ando S
Kyushu Nniv. Fukuoka Jpn
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Terasaki Fumio
Third Department of Internal Medicine, Osaka Medical College
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Terasaki F
大阪医科大学 第三内科
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Terasaki Fumio
大阪薬科大学 薬物治療学
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Kawamura Keishiro
Department Of Cardiology Sakakibara Heart Institute
-
Kawamura Keishiro
大阪医科大学 内科学iii
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Kawamura Keishiro
Third Division, Department of Internal Medicine, Osaka Medical College
-
Takeshita Akira
Research Institute Of Angiocardiology And Cardiovascular Clinic Faculty Of Medicine Kyushu Universit
-
Egashira Kensuke
Research Institute of Angiocardiology and Cardiovascular Clinic, Kyushu University
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安藤 真一
Division Of Cardiology Saiseikai Futsukaichi Hospital
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Terasaki Fumio
Third Department Of Internal Medicine Osaka Medical College
-
Terasaki Fumio
The Third Division Department Of Internal Medicine Osaka Medical College
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Matsumoto Takahiro
Research Institute of Angiocardiology and Cardiovascular Clinic, Faculty of Medicine, Kyushu Univers
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Kawamura Keishiro
Department Of Internal Medicine (iii) Osaka Medical College
-
Deguchi Hirofumi
Third Division, Department of Internal Medicine, Osaka Medical College
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Deguchi Hirofumi
Department Of Internal Medicine Iii Osaka Medical College
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Egashira Kensuke
Research Institute Of Angiocardiology And Cardiovascular Clinic Faculty Of Med. Kyushu University
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MATSUMOTO Takahiro
The Research Institute of Angiocardiology and Cardiovascular Clinic, Kyushu University
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Usui Makoto
Research Institute of Angiocardiology and Cardiovascular Clinic, Kyushu University
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Kawamura Keishiro
Third Department Of Internal Medicine Osaka Medical College
-
Usui Makoto
Department Of Cardiovascular Medicine Graduate School Of Medical Sciences Kyushu University
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Matsumoto Takahiro
Research And Development Center Stanley Electric Corporation
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Matsumoto Takahiro
The Research Institute Of Angiocardiology And Cardiovascular Clinic Kyushu University
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Deguchi Hirofumi
The 3rd Div. Dept.of Int.med. Osaka Medical College
-
Takeshita Akira
Research Institute Of A Ngiocardiology And Cardiovascular Clinic Faculty Of Medicine Kyushu Universi
-
Kawamura Keishiro
Third Division Department Of Internal Medicine Osaka Medical College
-
Deguchi Hirofumi
大阪医科大学 第3内科
-
Kawamura Keishiro
The 3rd Div. Dept.of Int.med. Osaka Medical College
-
Kawamura Keishiro
The Third Department Of Internal Medicine Osaka Medical College
-
Egashira Kensuke
Research Institute of Angiocardiology and Cardiovascular Clinic , Faculty of Med. Kyushu University
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