腸回転異常を伴った乳糜腹水症の1例

概要

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A case of 1 month old girl of chylousascites associated with malrotation of intestine was reported. The association of malrotation with chylousascites is very rare. This is second case in Japan as far as known. She was urgently sent to our hospital complaining of dyspnea with abdominal distention and loss of appetite. By the laboratory examinations leucocytosis and hypoproteinemia were presented. A diagnostic abdominal paracentesis obtained milky ascites and many fat globules and chylo-micron were found microscopically. The diagnosis of chylousascites was made. The ingredients of the ascites were protein 5.5g/dl, totallipid 2,180mg/dl, triglyceride 2,420mg/dl, phospholipid 122mg/dl and β-lipoprotein 1,005mg/dl. The Goldon's test showed 2.0% rouling out the proteinloosing entelopathy. Patient was treated by five times paracentesis and the low fat milk (Meiji No.810: protein 13.3g/100g, fat 3.5g/100g) for 100 days. Her course was uneventful and patient left the hospital after 18 weeks. It could be pointed out that in addition to the malrotation, the hypoplasia of the lymphatic system seems to play a part in this case. Low fat milk administration was very effective for this case.
日本小児外科学会の論文
1983-08-20