胆嚢原発の横紋筋肉腫の 1 例

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Although childhood rhabdomyosarcoma is relatively common, that of the gallbladder is extremely rare and only 2 adult cases were previously reported in the world literature. Recently we experienced a case of rhabdomyosarcoma arising from the gallbladder which is considered to be the first case in children. A 6-year-old girl was admitted with complaint of jaundice, fever and epigastric pain. At surgery, it was revealed that there were numerous botryoid masses in the gallbladder and common bile duct. The tumors were completely and easily removed with the gallbladder and the common duct and a hepaticojejunostomy was carried out. The postoperative diagnosis was embryonal rhabdomyosarcoma and there was no invasion toward the common bile duct histologically. She has been treated with combined radiotherapy and chemotherapy (VAC). There has been no evidence of recurrence or metastasis during the past 12 months. The long-term survival is expected because the complete excision was carried out at the early stage of the disease.
日本小児外科学会の論文