小児の炎症性肝外胆管狭窄症 : 胆道閉鎖の不全型?

概要

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A female child, 5 years and 5 months of age, who had had longstanding obstructive jaundice with hepatic dysfunction form the age of 6 months, underwent a Roux-Y hepaticojejunostomy after excision of the entire extrahepatic bile duct with severe periductal fiibrosis. At the time, liver biopsy already showed a progress of biliary cirrhosis with prominent ductal proliferation in the Glisson triad. Although good bile drainage to the intestine was obtained early after the operation, disappearance of jaundice and ascites with improvement of liver function has required a lapse of 2 years. The patient is now 13 years old and doing well with moderately impaired liver function. No esophageal varices have been seen by endoscopy lately. The clinical course and data are suggestive of an abortive form of biliary atresia.
日本小児外科学会の論文
1982-08-20