Susac's Syndrome: Beneficial Effects of Corticosteroid Therapy in a Japanese Case
スポンサーリンク
概要
- 論文の詳細を見る
Susacs syndrome is a rare disorder characterized by the triad of microangiopathy of the brain and retina with hearing loss. More than 50 affected individuals have been reported worldwide, all Caucasians. We herein identify the first Japanese patient with Susacs syndrome. A 36-year-old man developed recurrent subacute encephalopathy, bilateral sensorineural hearing loss, and retinal arteriolar occlusions, caused by microangiopathy from a year previously. T2-weighted MRI showed multiple high-signal lesions predominantly in the periventricular white matter. During the exacerbated phase both high-dose intravenous methylprednisolone and oral prednisone therapy produced beneficial effects. He showed definite remission within 2 years from the disease onset.(Internal Medicine 40: 135-139, 2001)
- 社団法人 日本内科学会の論文
著者
-
HASHIMOTO Yoichiro
the Department of Neurology
-
Uchino Makoto
The Departments Of Neurology
-
Uchino Makoto
The Department Of Neurology Kumamoto University School Of Medicine
-
Uyama Eiichiro
The Department Of Neurology Kumamoto University School Of Medicine
-
HASHIMOTO Yoichiro
Department of Neurology, Kumamoto City Hospital
-
YONEHARA Toshiro
Department of Neurology, Stroke Center, Saiseikai Kumamoto Hospital
-
TASHIMA Kazuhiro
the Department of Neurology, Kumamoto University School of Medicine
-
YONEHARA Toshiro
the Department of Neurology, Cerebrovascular Center, Saiseikai Kumamoto Hospital
-
Tashima Kazuhiro
The Department Of Neurology Kumamoto University School Of Medicine
-
Yonehara Toshiro
The Department Of Neurology Cerebrovascular Center Saiseikai Kumamoto Hospital
-
Hashimoto Yoichiro
The Department Of Neurology Kumamoto City Hospital
-
Hashimoto Yoichiro
The Department Of Neurology And Strokology Kumamoto City Hospital
関連論文
- The Severity of Minamata Disease Declined in 25 Years : Temporal Profile of the Neurological Findings Analyzed by Multiple Logistic Regression Model
- Inhibitory Effect of α-Tocopherol on Methylmercury-Induced Oxidative Steress
- Clinical Investigation of the Lesions Responsible for Sensory Disturbance in Minamata Disease
- Parkinsonian Symptoms as an Initial Manifestation in a Japanese Patient with Acquired Immunodeficiency Syndrome and Toxoplasma Infection
- Involvement of the Central Nervous System in Rheumatoid Arthritis : Its Clinical Manifestations and Analysis by Magnetic Resonance Imaging
- Transesophageal Echocardiography for Detection of Cardiac Diseases in Patients with Retinal Artery Occlusion
- Distribution of Dystrophin and Dystrophin-Associated Protein 43DAG(β-dystroglycan) in the Central Nervous System of Normal Controls and Patients with Duchenne Muscular Dystrophy
- Carotid Artery Disease in Patients with Retinal Artery Occlusion
- High Incidence of Thrombosis in Fabry's Disease
- Arg133Cys Mutation of Notch3 in Two Unrelated Japanese Families with CADASIL
- Hodgkin's Disease Preceded by Unique Neurological Symptoms
- Two Cases of Hemiballism-hemichorea with T1-weighted MR Image Hyperintensities in Patients with Hyperglycemia
- Progress of Diagnosis of Acute Stroke
- A Unique Case of Sporadic Creutzfeldt-Jacob Disease Presenting as Progressive Supranuclear Palsy
- Spontaneous Dissection Associated with Proximal Vertebral Artery Anomaly
- Recanalization of the middle cerebral artery after treatment with tissue plasminogen activator in a patient with embolic occlusion detected by transcranial color-flow imaging
- Change in the Age of Onset in Patients with Familial Amyloidotic Polyneuropathy Type I
- Hodgkin's Disease Preceded by Unique Neurological Symptoms
- Fibrinogen Kumamoto with an Aα Arg-19 to Gly Substitution Has Reduced Affinity for Thrombin Possible Relevance to Thrombosis
- Susac's Syndrome: Beneficial Effects of Corticosteroid Therapy in a Japanese Case
- Oral Intake 6 Months after Acute Ischemic Stroke
- A Unique Case of Sporadic Creutzfeldt-Jacob Disease Presenting as Progressive Supranuclear Palsy.
- Efficacy of Edaravone in Cardioembolic Stroke