Establishment of immortalized Schwann cells from Sandhoff mice and corrective effect of recombinant human β-hexosaminidase A on the accumulated GM2 ganglioside
スポンサーリンク
概要
著者
-
Tajima Youichi
Department Of Clinical Genetics The Tokyo Metropolitan Institute Of Medical Science Tokyo Metropolit
-
Kotani Masaharu
Department Of Clinical Genetics The Tokyo Metropolitan Institute Of Medical Science Tokyo Metropolit
-
Kotani M
Department Of Tumor Immunology The Tokyo Metropolitan Institute Of Medical Science
-
Ohsawa Mai
Department Of Clinical Genetics The Tokyo Metropolitan Institute Of Medical Science Tokyo Metropolit
関連論文
- Comparison of the effects of agalsidase alfa and agalsidase beta on cultured human Fabry fibroblasts and Fabry mice
- Clinical, biochemical, and cytochemical studies on a Japanese Salla disease case associated with a renal disorder
- Uptake of a Recombinant Human α-L-Iduronidase (laronidase) by Cultured Fibroblasts and Osteoblasts(Molecular and Cell Biology)
- Establishment of immortalized Schwann cells from Fabry mice and their low uptake of recombinant α-galactosidase
- Corrective effect on Fabry mice of yeast recombinant human α-galactosidase with N-linked sugar chains suitable for lysosomal delivery
- Egg envelope glycoprotein gp37 as a Xenopus homolog of mammalian ZP1, based on cDNA cloning
- Structural and biochemical studies on Pompe disease and a "pseudodeficiency of acid α-glucosidase"
- II-C-21 Morphological analysis of the effects of enzyme replacement therapy for Fabry model mice(THE 45TH ANNUAL MEETING OF THE JAPAN SOCIETY OF HISTOCHEMISTRY AND CYTOCHEMISTRY)
- Structural and immunocytochemical studies on α-N-acetylgalactosaminidase deficiency (Schindler/Kanzaki disease)
- Molecular and structural studies of the GM2 gangliosidosis O variant
- Ganglioside GT1b in Rat Brain Binds to p58,a Brain-Specific Sodium-Dependent Inorganic Phosphate Cotransporter:Expression Cloning with a Specific Monoclonal Antibody to Ganglioside GT1b-Binding Protein
- Differential distribution of ganglioside GM1 and sulfatide during the development of Xenoqus
- Evidence for Direct Binding of Intracellularly Distributed Ganglioside GM2 to Isolated Vimentin Intermediate Filaments in Normal and Tay-Sachs Disease Human Fibroblasts
- Establishment of immortalized Schwann cells from Sandhoff mice and corrective effect of recombinant human β-hexosaminidase A on the accumulated GM2 ganglioside
- Differential Distribution of Glycosphingolipid Antigens in the Central Nervous System (Recent Progresses in Carbohydrate Histochemistry)
- Biochemical and structural study on a S529V mutant acid α-glucosidase responsive to pharmacological chaperones
- Structural modeling of mutant α-glucosidases resulting in a processing/transport defect in Pompe disease
- Immunohistochemical Localization of Major Gangliosides in Rat Cerebellum.