A Case Report of von Recklinghausen's Disease with Tremendous Hypertrophy of Lower Extremities

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The patient, a 30 years old male, visited our clinic in June 1973, complained of gait disturbance and hoped to reduce his hypertrophied buttocks and lower limbs which gradually increased its volume during last 5 years.The pigmentations were presented on his face, trunk and all extremities. Roentgenograms revealed scoliosis, bone cysts, cortical defects and anterior angulation of tibia etc. Then angiograms of lower extremities were taken.As treatment, the extirpation of subcutaneous soft tissue including neurofibromatosis and the excision of its skin were done in antero-medial and in posterior parts of left leg in August and October, 1973. In operation, the bleeding from parenchyma was not so little to discomfort. The tumors were various in size and connected one another partly with nerve fibers. The appearance of tumors cut down was grayish and elastic. The tumors of Ca. 4kg. were extirpated. Microscopic examinations of these tumors showed schwannoma composed of numerous grown nerve fibers.
西日本整形・災害外科学会の論文